{"title":"巨大肾血管平滑肌脂肪瘤1例","authors":"S. Nawrocki, A. Lachowski","doi":"10.26715/jbms.34_2022_1_10","DOIUrl":null,"url":null,"abstract":"Renal Angiomyolipoma (AML), moreover known as a renal hamartoma, is a solid tumor with no malignant characteristics. The inheritance pattern of renal AML is autosomal dominant. If the lesion grows to a large size, a series of clinical manifestations and important complications might also occur. This research paper presents a case of huge renal AML in a 47-year-old lady, who visited the Emergency Department of Bahrain Defence Forces Hospital with right-sided abdominal pain of sudden onset. The patient underwent a total right nephrectomy. The resected mass was sized 10.5 x 13 x 14 cm. Postoperative histopathological examination confirmed the lesion as a huge renal AML. Due to the huge size of the tumor, it is crucial to record similar cases, along with their diagnosis and treatment. Keywords: Abdominal pain, Angiomyolipoma, Hamartoma, Kidney Neoplasms, Nephrectomy","PeriodicalId":85027,"journal":{"name":"Journal of the Bahrain Medical Society = Majallat Jam'iyat al-Atibba' al-Bahrayniyah","volume":"4 1","pages":""},"PeriodicalIF":0.0000,"publicationDate":"2022-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Giant Renal Angiomyolipoma: A Case Report\",\"authors\":\"S. Nawrocki, A. Lachowski\",\"doi\":\"10.26715/jbms.34_2022_1_10\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Renal Angiomyolipoma (AML), moreover known as a renal hamartoma, is a solid tumor with no malignant characteristics. The inheritance pattern of renal AML is autosomal dominant. If the lesion grows to a large size, a series of clinical manifestations and important complications might also occur. This research paper presents a case of huge renal AML in a 47-year-old lady, who visited the Emergency Department of Bahrain Defence Forces Hospital with right-sided abdominal pain of sudden onset. The patient underwent a total right nephrectomy. The resected mass was sized 10.5 x 13 x 14 cm. Postoperative histopathological examination confirmed the lesion as a huge renal AML. Due to the huge size of the tumor, it is crucial to record similar cases, along with their diagnosis and treatment. Keywords: Abdominal pain, Angiomyolipoma, Hamartoma, Kidney Neoplasms, Nephrectomy\",\"PeriodicalId\":85027,\"journal\":{\"name\":\"Journal of the Bahrain Medical Society = Majallat Jam'iyat al-Atibba' al-Bahrayniyah\",\"volume\":\"4 1\",\"pages\":\"\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2022-01-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Journal of the Bahrain Medical Society = Majallat Jam'iyat al-Atibba' al-Bahrayniyah\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.26715/jbms.34_2022_1_10\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Journal of the Bahrain Medical Society = Majallat Jam'iyat al-Atibba' al-Bahrayniyah","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.26715/jbms.34_2022_1_10","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 0
摘要
肾血管平滑肌脂肪瘤(AML)，又称肾错构瘤，是一种无恶性特征的实体瘤。肾性AML的遗传模式为常染色体显性。如果病变发展到较大，还可能出现一系列临床表现和重要的并发症。本文报告一位47岁的女士，因右侧突然腹痛到巴林国防军医院急诊科就诊，患严重肾性急性髓性白血病。病人接受了全右肾切除术。切除肿块大小为10.5 x 13 x 14 cm。术后组织病理学检查证实病变为巨大的肾性急性髓性白血病。由于肿瘤体积巨大，记录类似病例及其诊断和治疗是至关重要的。关键词:腹痛，血管平滑肌脂肪瘤，错构瘤，肾肿瘤，肾切除术
Renal Angiomyolipoma (AML), moreover known as a renal hamartoma, is a solid tumor with no malignant characteristics. The inheritance pattern of renal AML is autosomal dominant. If the lesion grows to a large size, a series of clinical manifestations and important complications might also occur. This research paper presents a case of huge renal AML in a 47-year-old lady, who visited the Emergency Department of Bahrain Defence Forces Hospital with right-sided abdominal pain of sudden onset. The patient underwent a total right nephrectomy. The resected mass was sized 10.5 x 13 x 14 cm. Postoperative histopathological examination confirmed the lesion as a huge renal AML. Due to the huge size of the tumor, it is crucial to record similar cases, along with their diagnosis and treatment. Keywords: Abdominal pain, Angiomyolipoma, Hamartoma, Kidney Neoplasms, Nephrectomy
求助内容：
应助结果提醒方式：
京公网安备 11010802042870号
