Case report of Hemophagocytic Syndrome complicated by septic shock

The incidence varies according to regions, with a predominance in pediatric patients. In adults, there has been an average age of onset at 50 years with a female predominance in a 1:7 with respect to the men [3]. An estimated worldwide incidence of 1.2 cases per million inhabitants. In Latin America, there is no standardized report that allows establishing epidemiological data, with an estimated survival of 38% one year after diagnosis [4] (Figure 1). However, this figure may be underestimated as it is a diagnosis of exclusion and due to the lack of specificity of the clinical picture.