与儿童矫正性心脏病相关的塑性支气管炎

IF 0.2 Q4 MEDICINE, GENERAL & INTERNAL
E. M. Kamaltynova, E. V. Krivoshchekov, Olga S. Yanulevich, Elena S. Kavardakova
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引用次数: 1

摘要

可塑性支气管炎(PB)是一种罕见的疾病,主要由于伴随的心脏或肺部病理,会导致成人和儿童气道阻塞,并伴有大型“橡胶”支气管铸型。它涉及渗出物或渗出物的组织,其形式为呼吸道。PB的死亡率达到50%。确切的流行病学数据尚不清楚。在大多数患者中,PB发生在重大疾病的背景下,有条件地可分为两组:心脏和血管疾病和肺部疾病的继发并发症。PB通常表现为呼吸困难、心动过速、缺氧、发烧和伴有气道阻塞的咳嗽。有时症状类似于哮喘或阻塞性支气管炎,伴有喘息和呼吸衰竭、饱和度降低(什么?)、发展为肺气肿的症状。所有现有的治疗方法都是有症状的。有希望的治疗方法是使用吸入的普通肝素和重组组织纤溶酶原激活剂(TAP)。本文介绍了一例5岁女孩PB的临床病例,其背景是纠正了心脏异常。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Пластический бронхит, ассоциированный с корригированным пороком сердца у ребенка
Plastic bronchitis (PB) is a rare disease that causes airway obstruction with large «rubber» bronchial casts in adults and children, mainly due to concomitant cardiac or pulmonary pathology. It involves the organization of exudate or transudate, which takes the form of the respiratory tract. Mortality with PB reaches 50%. Exact epidemiological data are not known. In most patients, PB occurs in the context of major diseases, which can be conditionally divided into two groups: heart and vascular disease and secondary complication of pulmonary diseases. Usually PB manifests with episodes of dyspnea, tachycardia, hypoxia, fever and cough associated with airway obstruction. Sometimes the symptoms resemble asthma or obstructive bronchitis, accompanied by wheezing and the symptoms of respiratory failure, decreasing of saturation (of what?), the development of pneumothorax. All existing methods of treatment are symptomatic. Promising methods of therapy are the use of inhaled unfractionated heparin and a recombinant tissue plasminogen activator (TAP). The article presents a clinical case of PB in a girl of 5 years with the background of corrected cardiac anomaly.
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来源期刊
Byulleten Sibirskoy Meditsiny
Byulleten Sibirskoy Meditsiny MEDICINE, GENERAL & INTERNAL-
CiteScore
0.70
自引率
50.00%
发文量
102
审稿时长
8 weeks
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