A case report and literature review of Abdominal Desmoplastic Small Round Cell Tumor

Objective To investigate the pathological characteristics, diagnosis, treatment decision and short-term curative effect of abdominal desmoplastic small round cell tumor. Methods The clinical data of a case of desmoplastic small round cell tumor admitted to Gansu provincial people′s Hospital in April 2018 were analyzed retrospectively.The clinical manifestations, pathological features, diagnosis and differential diagnosis, treatment and prognosis of desmoplastic small round cell tumor were summarized and analyzed. Results The patient was successfully treated with maximum tumor reduction.The operation time was 360 minutes.The estimated blood loss during operation was 200 ml, and no blood was transfused during operation.The abdominal drainage tube was removed on the 8th day after operation and the liver function recovered well.Postoperative pathology: (retroperitoneal) small round cell malignant tumor.Combined with clinical and immunohistochemical staining results: highly considered: desmoplastic small round cell tumor.The patient was discharged on the 16th day after operation.The patient was followed up for 4 months and the tumor recurred and liver metastasis.The follow-up period is now up to October 2018. Conclusion Desmoplastic small round cell tumor is a rare and highly malignant soft tissue small cell tumor with poor prognosis.Imaging examination and detection of tumor markers have no specificity and diagnose of it is difficult.Complete resection of the tumor and combined chemotherapy can improve the prognosis of the patients, but the prognosis is still not satisfactory, and more effective treatment decisions still need to be explored. Key words: Desmoplastic Small Round Cell Tumor; Chemotherapy; Histopathology