A Rare Presentation of Wegners Granulomatosis as Complete Heart Block

Cardiac involvement is seen in 6 to 25% Wegener’s granulomatosis, but very rarely it can involve the conduction system and manifest as complete heart block. Earlier most of the case reports were with systemic variant rather than a limited variant. We report a case of complete Heart Block (3rd degree) in a case of limited Wegner granulomatosis which was treated with Permanent Pacemaker Implantation. Complete AV block is a rare but treatable manifestation of cardiac involvement of wegners granulomatosis usually associated with early active systemic disease. All patients diagnosed with Wegener’s granulomatosis should be screened with a baseline electrocardiogram and a transthoracic echocardiogram to document cardiac involvement and alert clinicians to those at risk of further cardiac complications.