Heng Zhang, Ying Zheng, Gang Ning, Chuan Fu, Li Bao
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引用次数: 1
摘要
herlin - werner - wunderlich (HWW)综合征是一种罕见的复杂的女性泌尿生殖系统异常,具有多种解剖表现。由于梗阻,大多数HWW综合征患者需要手术治疗。治疗策略应针对每个患者的不同解剖变异而量身定制。因此,术前需要进行详细、全面的评估。在这篇综述中,我们描述了HWW综合征的胚胎学和临床表现,并讨论和说明了其术前不同的磁共振成像表现,以指导临床治疗。
Preoperative MRI presentations of Herlyn–Werner–Wunderlich syndrome
Herlyn–Werner–Wunderlich (HWW) syndrome is a rare complex female urogenital anomaly, with diverse anatomical presentations. Due to obstruction, most patients with HWW syndrome need to be addressed surgically. The treatment strategy should be tailored to the different anatomical variants of each patient. Therefore, a detailed and comprehensive preoperative evaluation is needed. In this review, we describe the embryology and clinical manifestations of HWW syndrome and discuss and illustrate its diverse preoperative magnetic resonance imaging presentations to guide clinical treatment.
期刊介绍:
Congenital Anomalies is the official English language journal of the Japanese Teratology Society, and publishes original articles in laboratory as well as clinical research in all areas of abnormal development and related fields, from all over the world. Although contributions by members of the teratology societies affiliated with The International Federation of Teratology Societies are given priority, contributions from non-members are welcomed.