结节性硬化症:介入放射科医生在治疗中的关键作用。

IF 0.7 Q4 RADIOLOGY, NUCLEAR MEDICINE & MEDICAL IMAGING

SA Journal of Radiology Pub Date : 2021-03-30 eCollection Date: 2021-01-01 DOI:10.4102/sajr.v25i1.2034

Puneet Garg, Anuradha Sharma, Heena Rajani, Apratim R Choudhary, Rajkumar Meena

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引用次数: 0

摘要

结节性硬化症(TSC)是一种常染色体显性的神经皮肤综合征，以多器官错构瘤为特征，本病例报告阐述了其特征性影像学特征。血管平滑肌脂肪瘤(AML)是TSC最常见的肾脏表现，在诊断时可能伴有危及生命的出血。选择性肾栓塞介入治疗是目前安全有效治疗肾性急性髓性白血病的首选治疗方法。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

Tuberous sclerosis complex: The critical role of the interventional radiologist in management.

查看原文本刊更多论文

Tuberous sclerosis complex: The critical role of the interventional radiologist in management.

Tuberous sclerosis complex (TSC) is an autosomal dominant neurocutaneous syndrome that is characterised by hamartomas in multiple organs, the characteristic imaging features of which are illustrated in this case report. Angiomyolipoma (AML) is the most common renal manifestation of TSC, which may present with life-threatening haemorrhage at the time of diagnosis. Interventional management with selective renal embolisation is currently the treatment of choice for the safe and effective management of ruptured renal AML.

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来源期刊

SA Journal of Radiology RADIOLOGY, NUCLEAR MEDICINE & MEDICAL IMAGING-

CiteScore

1.20

自引率

11.10%

发文量

审稿时长

16 weeks

期刊介绍： The SA Journal of Radiology is the official journal of the Radiological Society of South Africa and the Professional Association of Radiologists in South Africa and Namibia. The SA Journal of Radiology is a general diagnostic radiological journal which carries original research and review articles, pictorial essays, case reports, letters, editorials, radiological practice and other radiological articles.