保留主动脉瓣的手术治疗65岁成人瓣上主动脉狭窄1例。

Q3 Medicine

Korean Journal of Thoracic and Cardiovascular Surgery Pub Date : 2020-06-05 DOI:10.5090/kjtcs.2020.53.3.144

Hong Ju Shin, Jae Seung Shin

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引用次数: 0

摘要

瓣上主动脉瓣狭窄(SVAS)是一种罕见的先天性心脏病，通常与威廉姆斯综合征同时发生。在成人人群中，一些SVAS病例被报道发生在纯合子家族性高胆固醇血症患者中。然而，由于这种疾病的罕见性，对于SVAS没有标准的手术治疗。在这里，我们提出一个成功的手术治疗的情况下，使用自体切除主动脉瓣在一个65岁的SVAS患者。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

Aortic Valve-Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult.

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Aortic Valve-Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult.

Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.

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来源期刊

Korean Journal of Thoracic and Cardiovascular Surgery Medicine-Surgery

自引率

0.00%

发文量

审稿时长

36 weeks