病例系列的三个成人患者的特殊临床表现的噬血细胞淋巴组织细胞增多症。

4区医学 Q3 Medicine

Netherlands Journal of Medicine Pub Date : 2020-04-01

M Khairoun, F Meynen, W Vercoutere, H L Leavis

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引用次数: 0

摘要

巨噬细胞活化综合征(MAS)是一种继发形式的噬血细胞淋巴组织细胞病(HLH)。MAS-HLH是一种未被充分认识且危及生命的疾病，与多种疾病相关，包括结缔组织疾病和炎症性疾病。在这里，我们报告了三例由不同实体触发的MAS-HLH成人患者，包括系统性红斑狼疮、Griscelli综合征2型和成人发病Still's病。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

本刊更多论文

Case series of three adult patients with exceptional clinical presentations of haemophagocytic lymphohistiocytosis.

Macrophage activation syndrome (MAS) is a secondary form of haemophagocytic lymphohistiocytosis (HLH). MAS-HLH is an underrecognised and life-threatening condition associated with a heterogeneous group of diseases including connective tissue disease and inflammatory disorders. Here, we report three cases of adult patients with MAS-HLH triggered by different entities, including systemic lupus erythematosus, Griscelli syndrome type 2, and Adult onset Still's disease.

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来源期刊

Netherlands Journal of Medicine 医学-医学：内科

自引率

0.00%

发文量

审稿时长

6-12 weeks

期刊介绍： The Netherlands Journal of Medicine publishes papers in all relevant fields of internal medicine. In addition to reports of original clinical and experimental studies, reviews on topics of interest or importance, case reports, book reviews and letters to the editor are welcomed.