Klaus Steinbrück, Marcelo Enne, Reinaldo Fernandes, Jose M Martinho, Lúcio F Pacheco-Moreira
{"title":"活体肝移植治疗卡罗里病2例报告","authors":"Klaus Steinbrück, Marcelo Enne, Reinaldo Fernandes, Jose M Martinho, Lúcio F Pacheco-Moreira","doi":"10.5402/2011/106487","DOIUrl":null,"url":null,"abstract":"<p><p>Caroli's disease (CD) is a rare autosomal recessive disorder characterized by intrahepatic cystic dilatation of the bile ducts. Patients with bilobar or progressive disease may require orthotopic liver transplantation (OLT). In the MELD era, living donor liver transplantation (LDLT) raised as the ultimate treatment option for these patients, once their MELD score is usually low. Herein, we describe 2 cases of patients (a 2-year-old girl and a 19-year-old teenager) that successfully underwent LDLT as a treatment for diffuse CD. The good postoperative courses of the two cases indicate that LDLT is a feasible option in the treatment of this disorder, even in complicated or early age patients.</p>","PeriodicalId":89400,"journal":{"name":"ISRN surgery","volume":"2011 ","pages":"106487"},"PeriodicalIF":0.0000,"publicationDate":"2011-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.5402/2011/106487","citationCount":"4","resultStr":"{\"title\":\"Living Donor Liver Transplantation for Caroli's Disease: A Report of Two Cases.\",\"authors\":\"Klaus Steinbrück, Marcelo Enne, Reinaldo Fernandes, Jose M Martinho, Lúcio F Pacheco-Moreira\",\"doi\":\"10.5402/2011/106487\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Caroli's disease (CD) is a rare autosomal recessive disorder characterized by intrahepatic cystic dilatation of the bile ducts. Patients with bilobar or progressive disease may require orthotopic liver transplantation (OLT). In the MELD era, living donor liver transplantation (LDLT) raised as the ultimate treatment option for these patients, once their MELD score is usually low. Herein, we describe 2 cases of patients (a 2-year-old girl and a 19-year-old teenager) that successfully underwent LDLT as a treatment for diffuse CD. The good postoperative courses of the two cases indicate that LDLT is a feasible option in the treatment of this disorder, even in complicated or early age patients.</p>\",\"PeriodicalId\":89400,\"journal\":{\"name\":\"ISRN surgery\",\"volume\":\"2011 \",\"pages\":\"106487\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2011-01-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://sci-hub-pdf.com/10.5402/2011/106487\",\"citationCount\":\"4\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"ISRN surgery\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.5402/2011/106487\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"2011/4/27 0:00:00\",\"PubModel\":\"Epub\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"ISRN surgery","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.5402/2011/106487","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2011/4/27 0:00:00","PubModel":"Epub","JCR":"","JCRName":"","Score":null,"Total":0}
Living Donor Liver Transplantation for Caroli's Disease: A Report of Two Cases.
Caroli's disease (CD) is a rare autosomal recessive disorder characterized by intrahepatic cystic dilatation of the bile ducts. Patients with bilobar or progressive disease may require orthotopic liver transplantation (OLT). In the MELD era, living donor liver transplantation (LDLT) raised as the ultimate treatment option for these patients, once their MELD score is usually low. Herein, we describe 2 cases of patients (a 2-year-old girl and a 19-year-old teenager) that successfully underwent LDLT as a treatment for diffuse CD. The good postoperative courses of the two cases indicate that LDLT is a feasible option in the treatment of this disorder, even in complicated or early age patients.
求助内容：
应助结果提醒方式：
京公网安备 11010802042870号
