中枢神经系统的浅表性含铁血黄素沉着症。一份病例报告。

Acta neurologica Pub Date : 1994-06-01
F Maggioni, F Martinello, R Iavicoli, F Pietrogrande, C P Trevisan
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引用次数: 0

摘要

一例特发性浅表性含铁血黄素沉着症(SH)的中枢神经系统和文献回顾提出。患者有进行性小脑性共济失调、听力丧失、嗅觉丧失、痉挛性麻痹等症状,但无精神恶化。通过脑和脊髓MRI进行诊断,T2加权图像显示脊髓、延髓、脑桥、中脑、小脑和大脑半球的浅表低密度,这些图像被认为是SH的病理特征。反复的脊髓液检查呈阴性,提示明显的蛛网膜下腔出血的证据在诊断中不是必需的。对于病因不明的SH患者,尚无有效的治疗方法。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Superficial hemosiderosis of the central nervous system. A case report.

A case of idiopathic superficial hemosiderosis (SH) of the central nervous system and a review of the literature are presented. The patient suffered from progressive cerebellar ataxia, hearing loss, anosmia, spastic paraparesis, but no mental deterioration. The diagnosis was made with brain and spinal MRI, that showed in T2 weighted images superficial hypointensity of spinal cord, medulla oblungata, pons, mesencephalon, cerebellum and cerebral hemispheres, images that are considered pathognomonic of SH. Repeated spinal fluid examinations were negative, suggesting that evidence of overt subarachnoidal bleeding is not essential in the diagnosis. In patients with SH of unknown etiology no valid therapy is yet available.

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