诊断挑战：由于1型先天性肺气道畸形，一位年轻患者的Kommerell憩室和肺隔离的不寻常组合

Q4 Medicine

Radiology Case Reports Pub Date : 2025-06-30 DOI:10.1016/j.radcr.2025.05.109

Andre-Alonso Taco-Masias MD , Luz-Marina Pajares-Goicochea MD

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引用次数: 0

摘要

Kommerell憩室（KD）、肺隔离（PS）和1型先天性肺气道畸形（CPAM-1）同时发生是一种非常罕见的临床情况。我们提出的第一个记录的情况下，这三位一体的年轻患者。我们报告一名患有慢性咳嗽和吞咽困难的14岁女性，通过胸部CT和CT血管造影显示：34 mm KD伴左锁骨下动脉异常，同一肺段的叶内PS与cpam - 1型特征相关，主要与混合型cpam -隔离病变有关。这种独特的关联表明血管和肺发育异常之间有共同的胚胎起源。考虑到潜在的并发症，影像学检查和多学科管理至关重要。

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A diagnostic challenge: The unusual combination of Kommerell’s diverticulum and pulmonary sequestration due to type 1 congenital pulmonary airway malformation in a young patient

The simultaneous occurrence of Kommerell's diverticulum (KD), pulmonary sequestration (PS), and congenital pulmonary airway malformation type 1 (CPAM-1) represents an exceptionally rare clinical scenario. We present the first documented case of this triad in a young patient. We present a 14-year-old female with chronic cough and dysphagia underwent to thoracic CT and CT angiography revealing: 34 mm KD with aberrant left subclavian artery, Intralobar PS associated to CPAM-type1 features in the same pulmonary segment, mostly related to hybrid CPAM-sequestration lesion. This unique association suggests a shared embryological origin between vascular and pulmonary developmental anomalies. Imaging findings and multidisciplinary management are crucial given potential complications.

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来源期刊

Radiology Case Reports Medicine-Radiology, Nuclear Medicine and Imaging

CiteScore

1.10

自引率

0.00%

发文量

1074

审稿时长

30 days

期刊介绍： The content of this journal is exclusively case reports that feature diagnostic imaging. Categories in which case reports can be placed include the musculoskeletal system, spine, central nervous system, head and neck, cardiovascular, chest, gastrointestinal, genitourinary, multisystem, pediatric, emergency, women''s imaging, oncologic, normal variants, medical devices, foreign bodies, interventional radiology, nuclear medicine, molecular imaging, ultrasonography, imaging artifacts, forensic, anthropological, and medical-legal. Articles must be well-documented and include a review of the appropriate literature.