Stuti Chowdhary, Syed Kamran Asif, Aparna Williams
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Drug Induced Sleep Endoscopy in a Child with Poland's Syndrome: A Clinical Challenge.
Drug induced sleep endoscopy (DISE) is an accepted diagnostic tool to pinpoint sites of dynamic obstruction in sleep apnoea. However, the challenges increase manifold in a child with Poland's syndrome (PS), a congenital condition characterised by hypoplasia or agenesis of thoracic musculoskeletal elements, with rare limb anomalies. There are numerous risks associated with anaesthesia, including difficulties with ventilation and the potential for malignant hyperthermia. We describe a case of a child with Poland's syndrome, with sleep disordered breathing. The patient was taken up for DISE-guided surgery. To our best knowledge, this is the first case of Poland's syndrome described with respect to DISE in literature. We discuss the case and our experience - both surgical and anaesthesia related Poland's syndrome.
期刊介绍：
Indian Journal of Otolaryngology and Head & Neck Surgery was founded as Indian Journal of Otolaryngology in 1949 as a scientific Journal published by the Association of Otolaryngologists of India and was later rechristened as IJOHNS to incorporate the changes and progress.
IJOHNS, undoubtedly one of the oldest Journals in India, is the official publication of the Association of Otolaryngologists of India and is about to publish it is 67th Volume in 2015. The Journal published quarterly accepts articles in general Oto-Rhino-Laryngology and various subspecialities such as Otology, Rhinology, Laryngology and Phonosurgery, Neurotology, Head and Neck Surgery etc.
The Journal acts as a window to showcase and project the clinical and research work done by Otolaryngologists community in India and around the world. It is a continued source of useful clinical information with peer review by eminent Otolaryngologists of repute in their respective fields. The Journal accepts articles pertaining to clinical reports, Clinical studies, Research articles in basic and applied Otolaryngology, short Communications, Clinical records reporting unusual presentations or lesions and new surgical techniques. The journal acts as a catalyst and mirrors the Indian Otolaryngologist’s active interests and pursuits. The Journal also invites articles from senior and experienced authors on interesting topics in Otolaryngology and allied sciences from all over the world.
The print version is distributed free to about 4000 members of Association of Otolaryngologists of India and the e-Journal shortly going to make its appearance on the Springer Board can be accessed by all the members.
Association of Otolaryngologists of India and M/s Springer India group have come together to co-publish IJOHNS from January 2007 and this bondage is going to provide an impetus to the Journal in terms of international presence and global exposure.
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