核心护理结果分类系统在肝移植患者中的应用:回顾性病例研究。

IF 0.7 4区 医学 Q4 GASTROENTEROLOGY & HEPATOLOGY
Mingyan Shen, Zuxin Shi
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引用次数: 0

摘要

肝豆状核变性(HLD),也称为Wilson病,是一种常染色体隐性铜代谢疾病,由ATP7B基因突变引起。由于铜在肝脏中的排泄有缺陷,过量的铜会积聚在肝脏、大脑、肾脏和角膜等组织中。临床表现为肝功能障碍、运动障碍、精神症状以及肾脏和眼睛损害。肝移植通过用健康的供体肝脏代替患病的肝脏,解决了潜在的遗传缺陷,破坏了铜积累和全身损伤的循环,是目前治疗该疾病的唯一方法。本病例报告讨论一名17岁男性诊断为HLD一年,发展为严重肝功能衰竭并接受紧急肝移植。患者病情危重,术后护理的综合性和有效性对其预后至关重要。本案例研究采用了先前研究开发的肝移植核心护理结果分类系统,并根据患者的实际数据取得了满意的结果。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Application of a Core Care Nursing Outcomes Classification System for Liver Transplantation Patients: A Retrospective Case Study.

Hepatolenticular degeneration (HLD), also known as Wilson's disease, is an autosomal recessive disorder of copper metabolism caused by mutations in the ATP7B gene. Due to defective copper excretion in the liver, excess copper accumulates in tissues such as the liver, brain, kidneys, and corneas. Clinically, this manifests as liver dysfunction, motor disturbances, psychiatric symptoms, and damage to the kidneys and eyes. Liver transplantation, by replacing the diseased liver with a healthy donor liver, addresses the underlying genetic defect, disrupting the cycle of copper accumulation and systemic damage, and is currently the only curative treatment for the disease. This case report discusses a 17-year-old male diagnosed with HLD for one year who developed severe liver failure and underwent emergency liver transplantation. The patient's critical condition meant that the comprehensiveness and effectiveness of postoperative nursing care were crucial to his outcome. This case study utilized a core Nursing Outcomes Classification system for liver transplantation, previously developed through research, and achieved satisfactory results based on the actual data from the patient.

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来源期刊
Gastroenterology Nursing
Gastroenterology Nursing 医学-护理
CiteScore
1.10
自引率
12.50%
发文量
88
审稿时长
>12 weeks
期刊介绍: Gastroenterology Nursing: The Official Leader in Science and Practice delivers the information nurses need to stay ahead in this specialty. The journal keeps gastroenterology nurses and associates informed of the latest developments in research, evidence-based practice techniques, equipment, diagnostics, and therapy. The only professional, peer-reviewed nursing journal covering this area, Gastroenterology Nursing is an invaluable resource for current SGNA guidelines, new GI procedures, pharmacology, career development, and certification review. Its lively editorial style and illustrations make the journal a pleasure to read and consult. Official Journal of the Society of Gastroenterology Nurses and Associates and Canadian Society of Gastroenterology Nurses and Associates
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