{"title":"核心护理结果分类系统在肝移植患者中的应用:回顾性病例研究。","authors":"Mingyan Shen, Zuxin Shi","doi":"10.1097/SGA.0000000000000894","DOIUrl":null,"url":null,"abstract":"<p><p>Hepatolenticular degeneration (HLD), also known as Wilson's disease, is an autosomal recessive disorder of copper metabolism caused by mutations in the ATP7B gene. Due to defective copper excretion in the liver, excess copper accumulates in tissues such as the liver, brain, kidneys, and corneas. Clinically, this manifests as liver dysfunction, motor disturbances, psychiatric symptoms, and damage to the kidneys and eyes. Liver transplantation, by replacing the diseased liver with a healthy donor liver, addresses the underlying genetic defect, disrupting the cycle of copper accumulation and systemic damage, and is currently the only curative treatment for the disease. This case report discusses a 17-year-old male diagnosed with HLD for one year who developed severe liver failure and underwent emergency liver transplantation. The patient's critical condition meant that the comprehensiveness and effectiveness of postoperative nursing care were crucial to his outcome. This case study utilized a core Nursing Outcomes Classification system for liver transplantation, previously developed through research, and achieved satisfactory results based on the actual data from the patient.</p>","PeriodicalId":12666,"journal":{"name":"Gastroenterology Nursing","volume":" ","pages":""},"PeriodicalIF":0.7000,"publicationDate":"2025-04-22","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Application of a Core Care Nursing Outcomes Classification System for Liver Transplantation Patients: A Retrospective Case Study.\",\"authors\":\"Mingyan Shen, Zuxin Shi\",\"doi\":\"10.1097/SGA.0000000000000894\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Hepatolenticular degeneration (HLD), also known as Wilson's disease, is an autosomal recessive disorder of copper metabolism caused by mutations in the ATP7B gene. Due to defective copper excretion in the liver, excess copper accumulates in tissues such as the liver, brain, kidneys, and corneas. Clinically, this manifests as liver dysfunction, motor disturbances, psychiatric symptoms, and damage to the kidneys and eyes. Liver transplantation, by replacing the diseased liver with a healthy donor liver, addresses the underlying genetic defect, disrupting the cycle of copper accumulation and systemic damage, and is currently the only curative treatment for the disease. This case report discusses a 17-year-old male diagnosed with HLD for one year who developed severe liver failure and underwent emergency liver transplantation. The patient's critical condition meant that the comprehensiveness and effectiveness of postoperative nursing care were crucial to his outcome. This case study utilized a core Nursing Outcomes Classification system for liver transplantation, previously developed through research, and achieved satisfactory results based on the actual data from the patient.</p>\",\"PeriodicalId\":12666,\"journal\":{\"name\":\"Gastroenterology Nursing\",\"volume\":\" \",\"pages\":\"\"},\"PeriodicalIF\":0.7000,\"publicationDate\":\"2025-04-22\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Gastroenterology Nursing\",\"FirstCategoryId\":\"3\",\"ListUrlMain\":\"https://doi.org/10.1097/SGA.0000000000000894\",\"RegionNum\":4,\"RegionCategory\":\"医学\",\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q4\",\"JCRName\":\"GASTROENTEROLOGY & HEPATOLOGY\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Gastroenterology Nursing","FirstCategoryId":"3","ListUrlMain":"https://doi.org/10.1097/SGA.0000000000000894","RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"GASTROENTEROLOGY & HEPATOLOGY","Score":null,"Total":0}
Application of a Core Care Nursing Outcomes Classification System for Liver Transplantation Patients: A Retrospective Case Study.
Hepatolenticular degeneration (HLD), also known as Wilson's disease, is an autosomal recessive disorder of copper metabolism caused by mutations in the ATP7B gene. Due to defective copper excretion in the liver, excess copper accumulates in tissues such as the liver, brain, kidneys, and corneas. Clinically, this manifests as liver dysfunction, motor disturbances, psychiatric symptoms, and damage to the kidneys and eyes. Liver transplantation, by replacing the diseased liver with a healthy donor liver, addresses the underlying genetic defect, disrupting the cycle of copper accumulation and systemic damage, and is currently the only curative treatment for the disease. This case report discusses a 17-year-old male diagnosed with HLD for one year who developed severe liver failure and underwent emergency liver transplantation. The patient's critical condition meant that the comprehensiveness and effectiveness of postoperative nursing care were crucial to his outcome. This case study utilized a core Nursing Outcomes Classification system for liver transplantation, previously developed through research, and achieved satisfactory results based on the actual data from the patient.
期刊介绍:
Gastroenterology Nursing: The Official Leader in Science and Practice delivers the information nurses need to stay ahead in this specialty. The journal keeps gastroenterology nurses and associates informed of the latest developments in research, evidence-based practice techniques, equipment, diagnostics, and therapy. The only professional, peer-reviewed nursing journal covering this area, Gastroenterology Nursing is an invaluable resource for current SGNA guidelines, new GI procedures, pharmacology, career development, and certification review. Its lively editorial style and illustrations make the journal a pleasure to read and consult.
Official Journal of the Society of Gastroenterology Nurses and Associates and Canadian Society of Gastroenterology Nurses and Associates