皮肤纤维肉瘤突出并肌样分化1例-罕见。

Q3 Medicine

Journal of Oral and Maxillofacial Pathology Pub Date : 2024-10-01 Epub Date: 2024-12-31 DOI:10.4103/jomfp.jomfp_30_24

Nisha Shetty, Swati Sharma, Adarsh Kudva

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引用次数: 0

摘要

头颈部隆突性皮肤纤维肉瘤（DFSP）是一种罕见的局部浸润性低级别肉瘤，通常累及真皮和周围结构，发生于中年人。常见的临床表现是在躯干上发现缓慢扩大的硬化斑块，通常无症状。在这个病例报告中，我们报告了一个37岁的男性患者，他被诊断为典型的DFSP，并伴有肌样细胞分化，这是一种罕见的情况。在这里，我们讨论了临床病理特征和组织发生，可以帮助诊断和治疗这种情况。

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A case of dermatofibrosarcoma protuberance with myoid differentiation - A rare occurrence.

Dermatofibrosarcoma protuberans (DFSP) of the head and neck is a rare, locally infiltrative, low-grade sarcoma that typically involves the dermis and surrounding structures occurring in middle-aged adults. The common clinical presentation consists of a slowly enlarging, indurated plaque, usually asymptomatic, found on the trunk. In this case report, we present a case of a 37-year-old male patient with facial swelling which was diagnosed as classic DFSP along with myoid differentiation, which is a rare occurrence. Here, we have discussed the clinicopathologic features and histogenesis that can aid in the diagnosis and treatment of this condition.

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来源期刊

Journal of Oral and Maxillofacial Pathology Medicine-Otorhinolaryngology

CiteScore

1.40

自引率

0.00%

发文量

115

期刊介绍： The journal of Oral and Maxillofacial Pathology [ISSN:print-(0973-029X, online-1998-393X)] is a tri-annual journal published on behalf of “The Indian Association of Oral and Maxillofacial Pathologists” (IAOMP). The publication of JOMFP was started in the year 1993. The journal publishes papers on a wide spectrum of topics associated with the scope of Oral and Maxillofacial Pathology, also, ensuring scientific merit and quality. It is a comprehensive reading material for the professionals who want to upgrade their diagnostic skills in Oral Diseases; allows exposure to newer topics and methods of research in the Oral-facial Tissues and Pathology. New features allow an open minded thinking and approach to various pathologies. It also encourages authors to showcase quality work done by them and to compile relevant cases which are diagnostically challenging. The Journal takes pride in maintaining the quality of articles and photomicrographs.