Kutluhan Eren Hazır, Kerem Aydın Mutlugüleçler, İrfan Özgen, Burçin Abud, Cenk Sarı
{"title":"以室上性心动过速为表现的巨大转移性心内恶性纤维性肿瘤1例。","authors":"Kutluhan Eren Hazır, Kerem Aydın Mutlugüleçler, İrfan Özgen, Burçin Abud, Cenk Sarı","doi":"10.5543/tkda.2023.19310","DOIUrl":null,"url":null,"abstract":"<p><p>Solitary fibrous tumors (SFTs) are rare neoplasms originating from fibroblastic mesenchymal cells. This case report details a 43-year-old female patient with cardiac SFT, a rarity in the medical literature, who presented with palpitations and a known malignancy. Supraventricular tachycardia was diagnosed in the emergency department, and a subsequent echocardiography revealed a giant mass in the left atrium after sinus rhythm restoration. The mass, causing symptomatic severe mitral stenosis, necessitated surgical intervention. Pathological examination of the surgical specimens confirmed the diagnosis of SFT. Cardiac masses are extremely rare in clinical practice, and the literature on SFTs is primarily limited to case reports. More research is needed due to the scarcity of information on managing this condition.</p>","PeriodicalId":94261,"journal":{"name":"Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidir","volume":"52 8","pages":"611-614"},"PeriodicalIF":0.0000,"publicationDate":"2024-12-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Giant Metastatic Intracardiac Malignant Fibrous Tumor Presenting with Supraventricular Tachycardia: A Case Report.\",\"authors\":\"Kutluhan Eren Hazır, Kerem Aydın Mutlugüleçler, İrfan Özgen, Burçin Abud, Cenk Sarı\",\"doi\":\"10.5543/tkda.2023.19310\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Solitary fibrous tumors (SFTs) are rare neoplasms originating from fibroblastic mesenchymal cells. This case report details a 43-year-old female patient with cardiac SFT, a rarity in the medical literature, who presented with palpitations and a known malignancy. Supraventricular tachycardia was diagnosed in the emergency department, and a subsequent echocardiography revealed a giant mass in the left atrium after sinus rhythm restoration. The mass, causing symptomatic severe mitral stenosis, necessitated surgical intervention. Pathological examination of the surgical specimens confirmed the diagnosis of SFT. Cardiac masses are extremely rare in clinical practice, and the literature on SFTs is primarily limited to case reports. More research is needed due to the scarcity of information on managing this condition.</p>\",\"PeriodicalId\":94261,\"journal\":{\"name\":\"Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidir\",\"volume\":\"52 8\",\"pages\":\"611-614\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2024-12-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidir\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.5543/tkda.2023.19310\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidir","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.5543/tkda.2023.19310","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Giant Metastatic Intracardiac Malignant Fibrous Tumor Presenting with Supraventricular Tachycardia: A Case Report.
Solitary fibrous tumors (SFTs) are rare neoplasms originating from fibroblastic mesenchymal cells. This case report details a 43-year-old female patient with cardiac SFT, a rarity in the medical literature, who presented with palpitations and a known malignancy. Supraventricular tachycardia was diagnosed in the emergency department, and a subsequent echocardiography revealed a giant mass in the left atrium after sinus rhythm restoration. The mass, causing symptomatic severe mitral stenosis, necessitated surgical intervention. Pathological examination of the surgical specimens confirmed the diagnosis of SFT. Cardiac masses are extremely rare in clinical practice, and the literature on SFTs is primarily limited to case reports. More research is needed due to the scarcity of information on managing this condition.