颌下腺恶性上皮样血管瘤：病例报告

Q4 Medicine

Radiology Case Reports Pub Date : 2024-09-24 DOI:10.1016/j.radcr.2024.09.027

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引用次数: 0

摘要

上皮样血管脂肪瘤（血管周围上皮样细胞瘤）是一种罕见的间叶肿瘤，具有独特的细胞形态和非特异性的影像学表现。大多数报道的血管周围上皮样细胞瘤（PEComas）都是良性的；但在极少数情况下，PEComas 也可能是恶性的，并伴有肺、肝、结节和骨转移。我们报告了一例 40 岁男性右侧颌下腺 PEC 瘤恶性转移至骨骼、肺部和肝脏的病例。我们将讨论颌下腺转移性 PEC 瘤这一罕见疾病的诊断和治疗方案。

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Malignant epithelioid angiomyolipoma of the submandibular gland: A case report

An epithelioid angiomyolipoma (a perivascular epithelioid cell tumor) is a rare mesenchymal neoplasm with distinctive cellular morphology and nonspecific imaging appearances. Mostly reported perivascular epithelioid cell tumors (PEComas) are benign; however, rarely, PEComas can be malignant with pulmonary, hepatic, nodal, and osseous metastases. We present a case of a 40-year-old man with malignant right submandibular salivary gland PEComa, metastasized to the bones, lungs, and liver. We are going to discuss the diagnosis and management options of the rare disease of metastatic PEComa of the submandibular salivary gland.

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来源期刊

Radiology Case Reports Medicine-Radiology, Nuclear Medicine and Imaging

CiteScore

1.10

自引率

0.00%

发文量

1074

审稿时长

30 days

期刊介绍： The content of this journal is exclusively case reports that feature diagnostic imaging. Categories in which case reports can be placed include the musculoskeletal system, spine, central nervous system, head and neck, cardiovascular, chest, gastrointestinal, genitourinary, multisystem, pediatric, emergency, women''s imaging, oncologic, normal variants, medical devices, foreign bodies, interventional radiology, nuclear medicine, molecular imaging, ultrasonography, imaging artifacts, forensic, anthropological, and medical-legal. Articles must be well-documented and include a review of the appropriate literature.