阴囊和阴茎轴水肿:低 C1 抑制剂获得性血管性水肿的一种不常见初始表现。

Case Reports in Urology Pub Date : 2024-09-11 eCollection Date: 2024-01-01 DOI:10.1155/2024/9172329
Meghan V Matheny, Timothy Craig, Joseph Y Clark
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引用次数: 0

摘要

低 C1 抑制剂获得性血管性水肿(AAE-C1-INH)是一种罕见疾病,其特征是获得性缺乏 C1 酯酶抑制剂(C1-INH)。本病例报告描述了一名 79 岁的患者因阴囊、阴茎轴、左下肢和左上肢无痛性肿胀而到急诊科就诊,化验值符合获得性血管性水肿,但病史、检查或全身 PET 扫描均未发现淋巴或风湿性疾病。正确诊断 AAE-C1-INH 对于防止危及生命的气道损伤、确保正确治疗以及排除淋巴系统疾病作为 AAE-C1-INH 的病因至关重要。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Edema of the Scrotum and Penile Shaft: An Uncommon Initial Presentation of Acquired Angioedema With Low C1-Inhibitor.

Acquired angioedema with low C1-inhibitor (AAE-C1-INH) is a rare disorder characterized by an acquired deficiency in the C1 esterase inhibitor (C1-INH). This case report describes a 79-year-old patient presenting to the emergency department for painless swelling of his scrotum, penile shaft, and left lower and upper extremities with lab values consistent with acquired angioedema without identifiable lymphoreticular or rheumatic disorder on history, exam, or total body PET scan. Proper diagnosis of AAE-C1-INH is essential to prevent life-threatening airway compromise, ensure proper therapy, and exclude lymphoreticular disorders as the etiology of AAE-C1-INH.

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