囊性纤维化患儿护理和疗效方面的进展。

IF 2.8 3区医学 Q2 RESPIRATORY SYSTEM

Clinics in Chest Medicine Pub Date : 2024-04-30 DOI:10.1016/j.ccm.2024.03.006

Bob Z. Sun MD, MA , Gregory S. Sawicki MD, MPH

引用次数: 0

摘要

囊性纤维化（CF）是一种氯离子转运遗传性疾病，具有多系统表现，包括吸入性粘液、反复窦肺感染、阻塞性肺部疾病和胰腺外分泌功能不全。通过新生儿筛查进行早期诊断、及时提供营养支持、改善粘液纤毛清除率的慢性疗法以及肺部感染的及时治疗，改善了 CF 儿童的总体预后。针对儿童的新型囊性纤维化跨膜传导调节剂疗法的普及，将继续彻底改变儿科CF护理。然而，要优化所有CF患儿的护理和治疗效果，仍存在巨大挑战。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Advances in Care and Outcomes for Children with Cystic Fibrosis

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来源期刊

Clinics in Chest Medicine 医学-呼吸系统

CiteScore

9.10

自引率

1.80%

发文量

审稿时长

6-12 weeks

期刊介绍： Clinics in Chest Medicine updates those in the fields of anesthesia, critical care, and respiratory medicine on the latest trends in patient management, providing a sound basis for choosing the best treatment options. Published quarterly—in March, June, September, and December—each issue offers state-of-the-art reviews on a single topic, including diseases of air movement and airways, infectious lung disease, pulmonary vascular disease, sleep-related disorders, respiratory failure, and systemic disease.