A Case of Pregnant Woman with Severe Mitral Regurgitation Demonstrating Left Ventricular Non-compaction

Left ventricular non-compaction is a rare form of cardiomyopathy. It is characterized by a thin compacted epicardial layer and a noncompacted endocardial layer with significant wall trabeculations and intertrabecular recesses that communicate with the ventricular cavity. It could be either in isolated form or coexists with other congenital heart diseases including valvular heart disease. It is associated with congestive heart failure, life threatening cardiac arrhythmia and thromboembolic complications. Adult LVNC has a prevalence of 0.01-0.27%. Diagnostic workup includes echocardiography, contrast ventriculography, and CT/MRI. Cardiac magnetic resonance imaging provides greater sensitivity and specificity, with a noncompacted to compacted myocardium ratio of > 2.3. Here we present an isolated case of Left ventricular non-compaction in a 21-year-old female due to underlying heart failure, suspected of Chronic Rheumatic Heart Disease. There is no specific treatment for LVNC, therapeutic measures are used for patient symptom relief with consideration of implantable cardioverter defibrillator and cardiac transplantation.