隔离左腹内动脉：何时手术？

IF 0.9 Q4 CARDIAC & CARDIOVASCULAR SYSTEMS

Annals of Pediatric Cardiology Pub Date : 2024-01-01 Epub Date: 2024-05-24 DOI:10.4103/apc.apc_191_23

Samuel J H Parsons, Harry Nuttall, Alexander Jones

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引用次数: 0

摘要

右主动脉弓伴有从肺动脉分离出来的左心房动脉是一种极为罕见的先天性心脏畸形。我们描述了两例在 4 个月大和 7 个月大时成功手术的病例的处理方法和复杂的手术时机考虑，包括使用头颅超声作为指导决策的有用工具。我们还首次报道了这种缺陷与包含 LEF1 基因的 4q25 缺失的关联。

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Isolation of the left innominate artery: When to operate?

A right aortic arch with an isolated left innominate artery from the pulmonary artery is an exceedingly rare congenital cardiac malformation. We describe the management and complex surgical timing considerations in two such cases, successfully operated on day 4 and 7 months of age, including the use of cranial ultrasound as a helpful tool to guide decision-making. We also describe the first reported association of this defect with a 4q25 deletion encompassing the LEF1 gene.

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来源期刊

Annals of Pediatric Cardiology CARDIAC & CARDIOVASCULAR SYSTEMS-

CiteScore

1.40

自引率

14.30%

发文量

审稿时长

23 weeks