儿童急性腹部的罕见病因：肠道肌肉节段性缺失，病例报告和文献综述

IF 0.4 4区医学 Q4 SURGERY

Indian Journal of Surgery Pub Date : 2024-02-14 DOI:10.1007/s12262-024-04052-7

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引用次数: 0

摘要

摘要节段性肠肌缺失（SAIM）是一种罕见的儿童临床病理现象。SAIM 的病因尚未完全阐明。SAIM病例多见于新生儿和成人。本诊所收治了一名 10 岁女孩，主诉为急性腹痛，经药物治疗后症状仍未缓解。腹部超声波检查显示十二指肠、空肠和横结肠壁弥漫性增厚。左下腹有积液。鉴于腹胀无法缓解、急性腹痛和肠梗阻，医生对患者进行了中线开腹手术。纤维带压迫了空肠，其中一小段空肠出现缺血并被切除。该段空肠的组织病理学检查报告为 SAIM--粘膜和粘膜下组织病理学图像清晰，未见固有肌。

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A Rare Cause of Acute Abdomen in Children: Segmental Absence of the Intestinal Musculature, a Case Report and Literature Review

Abstract

Segmental absence of the intestinal musculature (SAIM) is a rare clinicopathological entity in childhood. The etiology of SAIM has not been fully elucidated. Cases of SAIM are mostly documented in neonate and adult population. A 10-year-old girl was admitted to our clinic with the complaint of acute abdominal pain that was not relieved on medical management. Ultrasound abdomen showed diffuse thickening of duodenum, jejunum, and transverse colon wall. There was fluid collection in the left lower abdomen. In view of unrelieved abdominal distention, acute abdominal pain, and intestinal obstruction, a midline laparotomy was performed. Fibrous bands were compressing the jejunum with a small jejunum segment that appeared ischemic and was resected. Histopathological examination of this jejunum segment was reported as SAIM—a clear cut histopathological picture of mucosa and sub-mucosa with no muscularis propria was seen.

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来源期刊

Indian Journal of Surgery SURGERY-

CiteScore

0.60

自引率

25.00%

发文量

412

审稿时长

6-12 weeks

期刊介绍： The Indian Journal of Surgery is the official publication of the Association of Surgeons of India that considers for publication articles in all fields of surgery. Issues are published bimonthly in the months of February, April, June, August, October and December. The journal publishes Original article, Point of technique, Review article, Case report, Letter to editor, Teachers and surgeons from the past - A short (up to 500 words) bio sketch of a revered teacher or surgeon whom you hold in esteem and Images in surgery, surgical pathology, and surgical radiology. A trusted resource for peer-reviewed coverage of all types of surgery Provides a forum for surgeons in India and abroad to exchange ideas and advance the art of surgery The official publication of the Association of Surgeons of India 92% of authors who answered a survey reported that they would definitely publish or probably publish in the journal again The Indian Journal of Surgery offers peer-reviewed coverage of all types of surgery. The Journal publishes Original articles, Points of technique, Review articles, Case reports, Letters, Images and brief biographies of influential teachers and surgeons. The Journal spans General Surgery, Pediatric Surgery, Neurosurgery, Plastic Surgery, Cardiothoracic Surgery, Vascular Surgery, Rural Surgery, Orthopedic Surgery, Urology, Surgical Oncology, Radiology, Anaesthesia, Trauma Services, Minimal Access Surgery, Endocrine Surgery, GI Surgery, ENT, Colorectal Surgery, surgical practice and research. The Journal provides a forum for surgeons from India and abroad to exchange ideas, to propagate the advancement of science and the art of surgery and to promote friendship among surgeons in India and abroad. This has been a trusted platform for surgons in communicating up-to-date scientific informeation to the community.