André Machado, Joana Dias, Ana Silva, Luís Meireles
{"title":"Chiari 1 型畸形:耳鸣的不寻常原因","authors":"André Machado, Joana Dias, Ana Silva, Luís Meireles","doi":"10.5935/0946-5448.20230002","DOIUrl":null,"url":null,"abstract":"<p><p>Chiari Malformations are a group of conditions defined in 1891 with 5 degrees being described. These malformations present with several symptoms such as cervical protrusion and are associated with hydrocephalus. Also, they can also present with different clinical signs and symptoms, such as deafness and tinnitus. We present a case of a 45-year-old man with unilateral tinnitus evaluated in otolaryngology office. No other symptoms on otolaryngological physical exam were detected in the audiogram performed it was described a significant unilateral sensorineural hearing loss. During the study of this patient, Magnetic Resonance Imaging was requested, showing a type I Chiari malformation. The patient was then observed by Ophthalmology, Neurology, and Neurosurgery. No other neurological symptoms of malformation Chiari syndrome or cranial nerve abnormalities were presented at the respective exam. The surgical management of these pathologies takes into account an adequate CSF and venous blood flow - that was seen in this patient, therefore, there was no surgical indication for decompression. The patient maintains its follow-up in the otolaryngology, neurology, and neurosurgery office, and tinnitus was minimized after prosthetic adaptation was recommended to optimize the quality of life, which was achieved.</p>","PeriodicalId":39842,"journal":{"name":"International Tinnitus Journal","volume":"27 1","pages":"6-9"},"PeriodicalIF":0.0000,"publicationDate":"2023-12-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":"{\"title\":\"Chiari Type 1 Malformation: An Unusual Cause of Tinnitus.\",\"authors\":\"André Machado, Joana Dias, Ana Silva, Luís Meireles\",\"doi\":\"10.5935/0946-5448.20230002\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Chiari Malformations are a group of conditions defined in 1891 with 5 degrees being described. These malformations present with several symptoms such as cervical protrusion and are associated with hydrocephalus. Also, they can also present with different clinical signs and symptoms, such as deafness and tinnitus. We present a case of a 45-year-old man with unilateral tinnitus evaluated in otolaryngology office. No other symptoms on otolaryngological physical exam were detected in the audiogram performed it was described a significant unilateral sensorineural hearing loss. During the study of this patient, Magnetic Resonance Imaging was requested, showing a type I Chiari malformation. The patient was then observed by Ophthalmology, Neurology, and Neurosurgery. No other neurological symptoms of malformation Chiari syndrome or cranial nerve abnormalities were presented at the respective exam. The surgical management of these pathologies takes into account an adequate CSF and venous blood flow - that was seen in this patient, therefore, there was no surgical indication for decompression. The patient maintains its follow-up in the otolaryngology, neurology, and neurosurgery office, and tinnitus was minimized after prosthetic adaptation was recommended to optimize the quality of life, which was achieved.</p>\",\"PeriodicalId\":39842,\"journal\":{\"name\":\"International Tinnitus Journal\",\"volume\":\"27 1\",\"pages\":\"6-9\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2023-12-04\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"1\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"International Tinnitus Journal\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.5935/0946-5448.20230002\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q3\",\"JCRName\":\"Medicine\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"International Tinnitus Journal","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.5935/0946-5448.20230002","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q3","JCRName":"Medicine","Score":null,"Total":0}
引用次数: 1
摘要
Chiari 畸形是 1891 年定义的一组疾病,共描述了 5 种程度的畸形。这些畸形表现出多种症状,如颈椎突出,并伴有脑积水。此外,它们还可能表现出不同的临床症状和体征,如耳聋和耳鸣。我们在耳鼻喉科诊室评估了一例单侧耳鸣的 45 岁男性患者。耳鼻咽喉科体检未发现其他症状,听力图显示单侧感音神经性听力损失明显。在对该患者进行检查期间,医生要求其接受磁共振成像检查,结果显示其患有 I 型奇异畸形。随后,眼科、神经内科和神经外科对患者进行了观察。各项检查均未发现其他畸形恰里综合征或颅神经异常的神经症状。这些病症的手术治疗需要考虑到充足的脑脊液和静脉血流,而该患者的情况正是如此,因此没有手术减压的指征。该患者一直在耳鼻喉科、神经内科和神经外科接受随访,在建议进行假体调适以优化生活质量后,耳鸣症状得到了缓解。
Chiari Type 1 Malformation: An Unusual Cause of Tinnitus.
Chiari Malformations are a group of conditions defined in 1891 with 5 degrees being described. These malformations present with several symptoms such as cervical protrusion and are associated with hydrocephalus. Also, they can also present with different clinical signs and symptoms, such as deafness and tinnitus. We present a case of a 45-year-old man with unilateral tinnitus evaluated in otolaryngology office. No other symptoms on otolaryngological physical exam were detected in the audiogram performed it was described a significant unilateral sensorineural hearing loss. During the study of this patient, Magnetic Resonance Imaging was requested, showing a type I Chiari malformation. The patient was then observed by Ophthalmology, Neurology, and Neurosurgery. No other neurological symptoms of malformation Chiari syndrome or cranial nerve abnormalities were presented at the respective exam. The surgical management of these pathologies takes into account an adequate CSF and venous blood flow - that was seen in this patient, therefore, there was no surgical indication for decompression. The patient maintains its follow-up in the otolaryngology, neurology, and neurosurgery office, and tinnitus was minimized after prosthetic adaptation was recommended to optimize the quality of life, which was achieved.
期刊介绍:
The International Tinnitus Journal is the first peer review journal to provide a forum for exchange of information of on-going basic and clinical science efforts for understanding tinnitus and its application to patient diagnosis and treatment. Subject areas to be covered range from fundamental theory to clinical applications.