[Congenital craniofacial malformation].

The authors report a classification of the congenital malformations of the neuro- and visceral cranium, showing that they are generated by chromosomal aberrations. The meningoencephaloceles with oculo-orbital manifestations are numerous and have to be differentiated from other cystic formations. The radiologic examination, in the most incidences is very important in their diagnosis. These pseudotumours can be treated only surgically in the neurosurgery departments. This treatment might be an emergency or not, as a function of their site and the state of the mucosae on the tegumenta covering them.