上消化道出血,Rapunzel综合征的罕见表现

Q4 Medicine
Carlos Torres-Salinas, David Anccasi-Hermoza
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引用次数: 0

摘要

胃肠牛黄在儿科年龄组有一个不寻常的表现,其临床表现主要与胃肠道梗阻性疾病有关,一般由头发和食物残渣组成。在少数病例中,可以看到牛黄结构从其通常的位置(胃)延伸到十二指肠、空肠、回肠甚至结肠,形成“长发公主尾巴”的外观。我们提出的情况下,一个7岁的女孩与非典型的最初介绍长发公主综合征,继发于毛流。患者以前没有精神病史,也没有在学校受到任何干扰的报告。她因上消化道出血被送进急诊室,随后需要输血。在她住院期间,进行了一次上消化道内镜检查,诊断为Rapunzel综合征,此外还存在两个Forrest II-C, III胃溃疡和胃窦和身体区域的严重红斑性胃炎。在没有这样的情况下开始治疗,为此必须通过手术将牛黄取出。因此,我们想指出深化某些方面的重要性,如这类患者的病史和背景,因为这是一种与行为和情绪改变有关的疾病;同样,记住不太常见的临床症状,如上消化道出血,但如果我们不及时采取行动,这些症状反过来可能是致命的。同样,在家庭的支持和心理学和/或精神病学的干预下,全面的治疗方法对预防复发至关重要。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Upper gastrointestinal bleeding, an unusual presentation of Rapunzel syndrome
Gastrointestinal bezoars in the pediatric age group have an unusual presentation, and their clinical manifestation is mainly associ- ated with obstructive conditions of the gastrointestinal tract, and are generally made up of hair and food debris. In a smaller num- ber, it has been seen that from its usual location, which is the stomach, bezoar structures could extend into the duodenum, jejunum, ileum, and even colon, giving the appearance of a “Rapunzel tail”. We present the case of a 7-year-old girl with an atypical initial presentation of Rapunzel syndrome, secondary to a trichobezoar. The patient did not have previous psychiatric history, nor reports of any disturbance at school. She was admitted to the emergency room due to upper gastrointestinal bleeding and required a subsequent transfusion of blood products. During her hospitalization, an up- per digestive endoscopy was performed, with the diagnosis of Rapunzel syndrome, in addition to the presence of two Forrest II-C, III gastric ulcers and severe erythematous gastritis in the region of the antrum and body. Medical treatment was started without suc- cess, for which the bezoar had to be surgically removed. Therefore, we want to point out the importance of deepening certain aspects such as the medical history and background in this type of patient, since it is a disorder linked to behavioral and mood alterations; likewise, remember the less frequent clinical symp- toms such as upper gastrointestinal bleeding, but which in turn can be lethal if we don’t act promptly. In the same way, the compre- hensive approach with the support of the family and the intervention of psychology and/or psychiatry is vital to prevent recurrences.
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来源期刊
Paediatria Croatica
Paediatria Croatica 医学-小儿科
CiteScore
0.20
自引率
0.00%
发文量
0
审稿时长
6-12 weeks
期刊介绍: In the inaugural 1956 issue of the journal, the editor Dr Feđa Fischer Sartorius outlined the journal''s vision and objectives saying that the journal will publish original papers on the development, pathology, and health care of children from the prenatal period to their final biological, emotional and social maturity. The journal continues this vision by publishing original research articles, clinical and laboratory observations, case reports and reviews of medical progress in pediatrics and child health.
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