肺动静脉畸形是儿童运动不耐受的一种病因:1例报告

IF 0.2 Q4 PEDIATRICS
Pierluigi Morreale, Veronica Notarbartolo, Giancarlo Allegro, Mario Giuseppe Vallone, Francesca Finazzo, Vincenzo Antona, Maria Fiorella Sanfilippo, Calogero Comparato
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引用次数: 0

摘要

儿童肺动静脉畸形(pavm)是一种罕见的病变,其特征是连接肺动脉和肺静脉的异常低阻力血管结构,导致肺内右至左分流。潜伏的发病和多变的体征和症状使诊断困难,特别是在儿童中。pavm可为单发或多发,先天性或获得性,高达47-80%的病例与遗传性出血性毛细血管扩张(HHT)有关。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Pulmonary arteriovenous malformation as a cause of exercise intolerance in children: a case report
Pulmonary arteriovenous malformations (PAVMs) in children are rare lesions characterized by abnormal low resistance vascular structures connecting a pulmonary artery to a pulmonary vein, resulting in an intrapulmonary right-to-left shunt. The insidious onset and variable signs and symptoms make diagnosis difficult, especially in children. PAVMs can be single or multiple, congenital or acquired, and up to 47-80% of cases are associated with hereditary hemorrhagic telangiectasia (HHT).
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来源期刊
CiteScore
0.40
自引率
0.00%
发文量
58
审稿时长
24 weeks
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