{"title":"肾上腺皮质癌:儿童腹膜后最罕见的肿瘤之一","authors":"D. Hanine, B. Rouijel, A. E. Baoudi, M. Kisra","doi":"10.31031/rpn.2021.05.000618","DOIUrl":null,"url":null,"abstract":"Adrenocortical Carcinoma (ACC) are rare tumors that have a bimodal distribution, the first peak is in children less than five years and the second around the fifth decade [1]. Although most adult ACC are non-functional, in the pediatric age group, nearly 95% are functional [2]. Virilization is the most common abnormality and Cushing’s syndrome and hyperaldosteronism are less frequent [3]. We begin the review with a clinical case of a 16-month-old infant, and then we will discuss this very rare pathology as well as its management.","PeriodicalId":153075,"journal":{"name":"Research in Pediatrics & Neonatology","volume":"4 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2021-04-29","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Adrenal Cortex Carcinoma: One of the Rarest Retroperitoneal Tumors in children\",\"authors\":\"D. Hanine, B. Rouijel, A. E. Baoudi, M. Kisra\",\"doi\":\"10.31031/rpn.2021.05.000618\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Adrenocortical Carcinoma (ACC) are rare tumors that have a bimodal distribution, the first peak is in children less than five years and the second around the fifth decade [1]. Although most adult ACC are non-functional, in the pediatric age group, nearly 95% are functional [2]. Virilization is the most common abnormality and Cushing’s syndrome and hyperaldosteronism are less frequent [3]. We begin the review with a clinical case of a 16-month-old infant, and then we will discuss this very rare pathology as well as its management.\",\"PeriodicalId\":153075,\"journal\":{\"name\":\"Research in Pediatrics & Neonatology\",\"volume\":\"4 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2021-04-29\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Research in Pediatrics & Neonatology\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.31031/rpn.2021.05.000618\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Research in Pediatrics & Neonatology","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.31031/rpn.2021.05.000618","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Adrenal Cortex Carcinoma: One of the Rarest Retroperitoneal Tumors in children
Adrenocortical Carcinoma (ACC) are rare tumors that have a bimodal distribution, the first peak is in children less than five years and the second around the fifth decade [1]. Although most adult ACC are non-functional, in the pediatric age group, nearly 95% are functional [2]. Virilization is the most common abnormality and Cushing’s syndrome and hyperaldosteronism are less frequent [3]. We begin the review with a clinical case of a 16-month-old infant, and then we will discuss this very rare pathology as well as its management.
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