Congenitally missing maxillary central incisor or solitary median maxillary central incisor?

Tooth agenesis is not a rare phenomenon. Most often, the tooth that shows agenesis is the maxillary lateral incisor or the third molars. Agenesis of maxillary central incisor is an extremely rare phenomenon. A case of congenital absence of maxillary central incisor in a 42-year-old, otherwise healthy individual is being presented. When one encounters a case, it is important that it is differentiated from the other serious form of the disease which is solitary median maxillary central incisor syndrome.