Sonali Verma, A. Agrawal, Chirag Verma, Vanny Arora, M. Narang
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引用次数: 1
摘要
一名11岁女童，表现为全身肿胀、腹水及肝肿大。近5年来有反复稀便病史。初步检查发现腹水和肝肿大。血清蛋白在正常范围内。初始超声示肝脏第七段等回声占位性病变伴腹水。超声多普勒显示右肝静脉血流减弱。5天后腹水突然好转，复查超声显示三条肝静脉及下腔静脉均通畅。腹部CECT显示肝脏第七段血管瘤，尺寸为2.1 X 2.6 X 1.36 cm，脂肪肝合并腹水合并肠系膜淋巴结病。因身材矮小及有腹泻史，测定血清ttg水平为372U/ml(正常0 ~ 20 U/ml)。活检证实为乳糜泻。因此，乳糜泻的诊断为肝静脉因血管瘤或血栓引起的一过性阻塞。毕业论文关键词:白花;腹水;乳糜泻
An 11 year old female child presented with generalized body swelling, ascites and hepatomegaly. She had history of recurrent loose stools since last 5 years. Initial work up revealed ascites, and hepatomegaly. Serum proteins were within normal limits. Initial USG revealed isoechoeic space occupying lesion in segment VII of liver with ascites. USG Doppler revealed attenuation of blood flow in right hepatic vein. Ascites suddenly improved after 5 days, repeat USG revealed that all three hepatic veins and inferior vena cava were patent. CECT abdomen showed hemangioma measuring 2.1 X 2.6 X 1.36 cm in segment VII of liver with fatty liver with ascites with mesenteric lymphadenopathy. Serum tTGlevel carried out because of short stature and history of diarrhea was 372U/ml (normal 0-20 U/ml). Celiac disease was confirmed on biopsy. Hence the diagnosis of celiac disease with transient obstruction of hepatic veins due to hemangioma or thrombus. Keywords: Budd Chiari; Ascites; Celiac disease
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