成人Bannayan-Riley-Ruvalcaba综合征的麻醉考虑:1例报告。

IF 0.5

A&A Practice Pub Date : 2023-07-01 DOI:10.1213/XAA.0000000000001690

Catherine M Pivalizza, Hayden B Jefferies, Evan G Pivalizza

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引用次数: 1

摘要

Bannayan-Riley-Ruvalcaba综合征是PTEN(磷酸酶和紧张素同源)误构瘤肿瘤综合征的一部分，成人患者的麻醉考虑尚未得到很好的描述。由于患者可能需要手术治疗相关的肌肉骨骼、肠道、肿瘤或软组织肿块，因此了解麻醉的影响是必要的。考虑到大头畸形和口腔/下咽淋巴管瘤组织的积累，气道管理可能具有挑战性。本报告描述了一个典型的特征，不可靠的外部气道解剖和发育迟缓，这妨碍了清醒气道管理技术。使用高流量鼻吸氧和视频喉镜检查气道。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Anesthetic Considerations for an Adult With Bannayan-Riley-Ruvalcaba Syndrome: A Case Report.

Anesthetic considerations for adults with Bannayan-Riley-Ruvalcaba syndrome, part of the PTEN (phosphatase and tensin homolog) hamartoma tumor syndrome, are not well described. As patients may require surgical intervention for associated musculoskeletal, intestinal, oncologic, or soft tissue masses, knowledge of implications of anesthesia is necessary. Airway management may be challenging given macrocephaly and accumulation of lymphangiomatous tissue in the oro/hypopharynx. This report describes a patient with typical features, nonreassuring external airway anatomy, and developmental delay, which precluded an awake airway management technique. The airway was secured with the use of high-flow nasal oxygen and videolaryngoscopy.

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来源期刊

A&A Practice ANESTHESIOLOGY-

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期刊介绍： A & A Case Reports, our new online journal publishing Case Reports, related Editorial Commentary, and Correspondence. Anesthesia & Analgesia 1 and Anesthesiology 2 recently announced that they were suspending publication of Case Reports. One reason is that Case Reports typically reduce the Impact Factor of a journal because they are rarely cited. Regardless of the merits of Impact Factor as a metric of journal worth, journals and their editors necessarily consider Impact Factor in strategic planning. At the same time, Case Reports are appreciated by readers for describing “real life” management of difficult or unusual cases not often encountered by practitioners. In a recent issue of Anesthesia & Analgesia, Steven Shafer1 identified many Case Reports whose publication launched productive careers dedicated to solving the puzzle posed by an unusual observation in a single patient.