多中心网状组织细胞增生症(Mrh):一例罕见的破坏性关节炎。

Q3 Medicine

Journal of Ayub Medical College, Abbottabad : JAMC Pub Date : 2023-04-01 DOI:10.55519/JAMC-02-9261

Saira Bano, Tayyeba Khursheed, Mohammad Khalid Bosan, Sadia Khurshid

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引用次数: 0

摘要

多中心网状组织细胞增多症是一种罕见的疾病，病因不明，主要影响皮肤和关节。没有专门用于诊断的实验室调查。诊断可以在临床和组织病理学的基础上作出。目前对治疗方法尚无共识。我们报告一例来自巴基斯坦的经典表现，甲氨蝶呤和低剂量类固醇治疗效果良好。及时诊断和早期治疗可以避免严重的残疾。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Multicentric Reticulohistiocytosis (Mrh): A Case Report On A Rare Destructive Arthritis.

Multicentric Reticulohistiocytosis is a rare disorder of unknown aetiology which affects skin and joints predominantly. There are no specific laboratory investigations for diagnosis. Diagnosis can be made clinically and on a histopathological basis. There is no consensus on treatment. We report a case from Pakistan with classical presentation who did well on methotrexate and low dose steroids. Prompt diagnosis and early treatment may save from significant disability.

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来源期刊

Journal of Ayub Medical College, Abbottabad : JAMC Medicine-Medicine (all)

CiteScore

0.80

自引率

0.00%

发文量

304