Adaptation of home nocturnal hemodialysis for a patient with epidermolysis bullosa: A call to personalized care!

IF 1.2 4区医学 Q3 UROLOGY & NEPHROLOGY

Hemodialysis International Pub Date : 2023-04-13 DOI:10.1111/hdi.13086

Rose Faratro, Christopher T. Chan

引用次数: 0

Abstract

Epidermolysis bullosa (EB) is a genetic disease characterized by skin fragility presenting with blistering and skin erosions. Recurrent skin infections are noted to be associated with the pathogenesis of IgA nephropathy. End stage kidney disease (ESKD) is a rare complication in patients with EB (Ducret F., et al., Nephrol Ther, 2008). Kidney replacement therapy is very challenging in this vulnerable patient population (Fine JD. et al., Am J Kidney Dis, 2004). Herein, we describe the adaptations to our home nocturnal hemodialysis training and operations to facilitate a patient with EB and ESKD to undergo personalized home nocturnal hemodialysis therapy.

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大疱性表皮松解症患者适应家庭夜间血液透析:呼唤个性化护理!

大疱性表皮松解症(EB)是一种遗传性疾病，以皮肤脆弱为特征，表现为起泡和皮肤糜烂。反复皮肤感染被认为与IgA肾病的发病机制有关。终末期肾病(ESKD)是EB患者中一种罕见的并发症(Ducret F.等，Nephrol Ther, 2008)。肾脏替代疗法在这一弱势患者群体中非常具有挑战性(Fine JD。et al.， Am J Kidney Dis, 2004)。在此，我们描述了适应我们的家庭夜间血液透析培训和操作，以促进EB和ESKD患者接受个性化的家庭夜间血液透析治疗。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Hemodialysis International UROLOGY & NEPHROLOGY-

CiteScore

2.50

自引率

0.00%

发文量

审稿时长

6-12 weeks

期刊介绍： Hemodialysis International was originally an annual publication containing the Proceedings of the International Symposium on Hemodialysis held in conjunction with the Annual Dialysis Conference. Since 2003, Hemodialysis International is published quarterly and contains original papers on clinical and experimental topics related to dialysis in addition to the Annual Dialysis Conference supplement. This journal is a must-have for nephrologists, nurses, and technicians worldwide. Quarterly issues of Hemodialysis International are included with your membership to the International Society for Hemodialysis. The journal contains original articles, review articles, and commentary to keep readers completely updated in the field of hemodialysis. Edited by international and multidisciplinary experts, Hemodialysis International disseminates critical information in the field.