Late Shone complex: A case report and literature review

Abstract

Shone complex is a very rare congenital heart disease made of coarctation of aorta, parachute mitral valve, supravalvular mitral ring and subaortic stenosis. Since its first description by Shone et al., in 1963, literature comes from isolated case reports mainly in children. Herein, a 33-year old lady with Shone complex is presented. She had had repair of coarctation of aorta at the age of 5 and mitral valve replacement, resection of subaortic membrane and left venricular myectomy at the age of 33. Surgery of Shone complex is expected to yield good outcome if undertaken before the onset of pulmonary hypertension.