Hemophilic Pseudotumor of the Distal Phalanx

Q3 Medicine
A. Afshar, A. Tabrizi
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引用次数: 0

Abstract

Introduction: Haemophilia is one of the hereditary recessive diseases linked to sex-induced coagulation disorder and is characterized by bleeding episodes. This report presents a rare involvement of the distal phalanx hemophilic pseudotumor. Case Presentation: A 21-year-old man was crushed by a closing door 18 months before. The distal phalanx was fractured, and a large hematoma developed under the nail plate, which separated the nail plate from its bed. Eighteen months after the injury, plain radiographs demonstrated an expansile lesion with extensive destruction of the distal phalanx. Regarding the patient’s history and abnormal clotting tests, the development of a hemophilic pseudotumor was considered at the distal phalanx due to the enlarging nature of the coagulum, which induced compression and pressure necrosis on the adjacent bone and structures. Conclusions: Hemophilic pseudotumors in the small bones are rarely reported. After a minor traumatic injury in hand, exact management and coagulopathy control are important to prevent further complications.
远端指骨血友病假瘤
血友病是一种与性致凝血障碍相关的遗传性隐性疾病,其特征是出血发作。本文报告一例罕见的远端指骨血友病假瘤。病例介绍:18个月前,一名21岁男子被关闭的门压死。远端指骨骨折,钉板下形成大血肿,使钉板与床分离。损伤后18个月,x线平片显示远端指骨广泛破坏,病变呈扩张性。根据患者的病史和异常的凝血试验,由于凝血的扩大性质,导致邻近骨和结构的压迫和压力性坏死,考虑在远端指骨发生血友病假瘤。结论:小骨内血友病性假肿瘤报道较少。手部轻微创伤后,精确的治疗和凝血功能的控制对于防止进一步的并发症是很重要的。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
Shiraz E Medical Journal
Shiraz E Medical Journal Medicine-Medicine (all)
CiteScore
1.00
自引率
0.00%
发文量
63
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