[Anesthetic problems of epidermolysis bullosa dystrophica. Apropos of a case].

Abstract

Epidermolysis bullosa is a group of hereditary diseases of the skin that may also involve mucous membranes, particularly of the oropharynx and oesophagus. The common primary feature is the formation of blisters following even trivial trauma. During the management of anaesthesia, it is critical that trauma to the skin and mucous membranes be avoided or minimized in these patients. We report the case of a 3-year-old child who had two surgeries and discuss the anaesthetic implications of this disease.