Double trouble-unilateral lung agenesis with obstructed infracardiac total anomalous pulmonary venous connection: A rare association with successful outcome.

Abstract

Lung agenesis associated with congenital heart disease is a rare and serious malformation that requires immediate medical attention. If not addressed with preplanned surgical and medical support, it can often lead to mortality. This report describes an unusual case of a 2-month-old male infant with left lung agenesis and obstructed infracardiac total anomalous pulmonary venous connection. The infant presented with congestive heart failure, dominated by symptoms of obstruction and pulmonary hypertension. We detail the successful surgical intervention and postoperative outcomes for this rare association.