Ectopic clival craniopharyngioma.

IF 2.6 3区 医学 Q2 CLINICAL NEUROLOGY
Golnaz Lotfian, Akram Al-Warqi, Santhosh Gaddikeri, Miral D Jhaveri, Surjith Vattoth
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引用次数: 0

Abstract

Craniopharyngiomas are rare, benign tumors with a bimodal age distribution, typically found in children and older adults. They arise along the craniopharyngeal tract, often in the intra- or suprasellar regions, and may compress adjacent structures, causing diverse symptoms. Diagnosis is primarily MRI-based, revealing heterogeneous mass with cystic and solid elements. Chordoma, another rare tumor, arises from notochordal remnants, often in the sacrum or clivus, and displays distinct imaging characteristics like T2 hyperintensity and bony destruction. This report discusses a rare ectopic clival craniopharyngioma in an 11-year-old- the youngest case reported in the literature to our knowledge -extending from the sellar to the clival region. Noteworthy imaging findings included T1 hyperintensity and a downward growth pattern along the expected Rathke pouch course, helping distinguish it from chordoma.

异位斜坡颅咽管瘤。
颅咽管瘤是一种罕见的良性肿瘤,具有双峰年龄分布,通常见于儿童和老年人。它们沿颅咽道出现,常位于鞍内或鞍上区域,并可压迫邻近结构,引起各种症状。诊断主要以mri为基础,显示具有囊性和实性成分的非均匀肿块。脊索瘤是另一种罕见的肿瘤,起源于脊索残余,常发生在骶骨或斜坡,表现出明显的成像特征,如T2高强度和骨破坏。本报告讨论一例罕见的异位斜坡颅咽管瘤,患者为11岁,是我们所知的文献中最年轻的病例,从鞍区延伸到斜坡区。值得注意的影像学表现包括T1高强度和沿预期Rathke袋程向下生长模式,有助于与脊索瘤区分。
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来源期刊
Neuroradiology
Neuroradiology 医学-核医学
CiteScore
5.30
自引率
3.60%
发文量
214
审稿时长
4-8 weeks
期刊介绍: Neuroradiology aims to provide state-of-the-art medical and scientific information in the fields of Neuroradiology, Neurosciences, Neurology, Psychiatry, Neurosurgery, and related medical specialities. Neuroradiology as the official Journal of the European Society of Neuroradiology receives submissions from all parts of the world and publishes peer-reviewed original research, comprehensive reviews, educational papers, opinion papers, and short reports on exceptional clinical observations and new technical developments in the field of Neuroimaging and Neurointervention. The journal has subsections for Diagnostic and Interventional Neuroradiology, Advanced Neuroimaging, Paediatric Neuroradiology, Head-Neck-ENT Radiology, Spine Neuroradiology, and for submissions from Japan. Neuroradiology aims to provide new knowledge about and insights into the function and pathology of the human nervous system that may help to better diagnose and treat nervous system diseases. Neuroradiology is a member of the Committee on Publication Ethics (COPE) and follows the COPE core practices. Neuroradiology prefers articles that are free of bias, self-critical regarding limitations, transparent and clear in describing study participants, methods, and statistics, and short in presenting results. Before peer-review all submissions are automatically checked by iThenticate to assess for potential overlap in prior publication.
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