Sebastian Molina-Rios, Leonardo Galindo, Diana Gil Calderón, Jose Yate, Manuela Rubio, Luis Javier Cajas-Santana
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引用次数: 0
Abstract
Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) is a group of inflammatory conditions that can potentially affect multiple systems, with respiratory involvement being a common manifestation. Pulmonary emphysema as a sole manifestation is extremely rare. We report a case series of three patients diagnosed with AAV as a potential cause of pulmonary emphysema. Additionally, we conducted a systematic review of the literature to explore this association.
期刊介绍:
Clinical Rheumatology is an international English-language journal devoted to publishing original clinical investigation and research in the general field of rheumatology with accent on clinical aspects at postgraduate level.
The journal succeeds Acta Rheumatologica Belgica, originally founded in 1945 as the official journal of the Belgian Rheumatology Society. Clinical Rheumatology aims to cover all modern trends in clinical and experimental research as well as the management and evaluation of diagnostic and treatment procedures connected with the inflammatory, immunologic, metabolic, genetic and degenerative soft and hard connective tissue diseases.