Two cases of bronchial artery aneurysms in patients with long-standing precapillary pulmonary hypertension

IF 2.4 Q2 RESPIRATORY SYSTEM
Taku Komori , Takahiro Sato , Ichizo Tsujino , Daisuke Tamatsuki , Shuhei Yoshikawa , Hideki Shima , Junichi Nakamura , Ryo Morita , Daisuke Abo , Satoshi Konno
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引用次数: 0

Abstract

Bronchial artery aneurysm (BAA) is a rare but increasingly recognized condition due to advances in imaging. We report two cases of BAA in patients with long-standing pulmonary hypertension. Case 1 is a 30-year-old man with idiopathic peripheral pulmonary artery stenosis diagnosed at age 23. He developed a slightly dilated bronchial artery, which later enlarged, leading to bronchial artery embolization. Case 2 is a 30-year-old woman with pulmonary arterial hypertension diagnosed at age 3. Multiple BAAs were identified at age 24, and progressive enlargement was observed at age 28. Due to lesion complexity, she remains under careful observation.
支气管动脉瘤伴长期毛细血管前肺动脉高压2例
支气管动脉动脉瘤(BAA)是一种罕见的疾病,但由于影像学的进步,越来越多的人认识到这种疾病。我们报告两例长期肺动脉高压患者的BAA。病例1是一名30岁男性,在23岁时被诊断为特发性肺外周动脉狭窄。他的支气管动脉轻微扩张,后来扩大,导致支气管动脉栓塞。病例2是一名30岁女性,在3岁时被诊断为肺动脉高压。24岁时发现多个baa, 28岁时观察到进行性扩大。由于病变复杂,她仍需仔细观察。
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来源期刊
Respiratory investigation
Respiratory investigation RESPIRATORY SYSTEM-
CiteScore
4.90
自引率
6.50%
发文量
114
审稿时长
64 days
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