Linear Scleroderma En Coup de Sabre: A Case Series With Eyelid Involvement and Management.

Abstract

Linear scleroderma en coup de sabre is a rare subtype of localized scleroderma. It is typically characterized by linear sclerosis and atrophy of the skin and underlying dermis affecting the frontoparietal region above the brow. The linear sclerotic lesions rarely extend into the upper eyelid. In this case series, the authors describe the presentation of 3 en coup de sabre cases, in particular the associated eyelid and adnexal findings which include upper eyelid skin fibrosis, sulcus hollowing, and eyelid retraction. The authors also describe the range of reconstructive treatment options in the remission phase with a combination of autologous fat transfer, injectable filler, eyelid retraction repair, and contralateral ptosis repair to improve facial symmetry and cosmesis of en coup de sabre lesions on the forehead, brow and eyelid region.