Luciano Maria Catalfamo, Danilo De Rinaldis, Carla Nava, Francesco Sbano, Francesco Saverio De Ponte, Calogero Scozzaro
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引用次数: 0
Abstract
Bean syndrome (BS) is a rare congenital angiomatosis affecting multiple organ systems. The exact etiology is still not well-known. About 200 cases with heterogeneous clinical presentations have been reported worldwide. BS predominantly presents with characteristic multifocal mucocutaneous lesions and often leads to iron-deficiency anemia caused by occult blood loss from the gastrointestinal tract. Apart from the mucocutaneous and gastrointestinal tract involvement, this syndrome may rarely affect the craniofacial region in the form of multiple venous anomalies, characterized by being button-like, with a bluish tint, covered by skin, called "Blue Nevus". Patients often approach a dermatologist or gastroenterologist for treatment and this entity is usually less known among maxillofacial surgeons. This article describes two consecutive cases of BS affecting the craniofacial district, with the aim of spreading greater awareness about this syndrome in the maxillofacial field.
期刊介绍：
Indian Journal of Otolaryngology and Head & Neck Surgery was founded as Indian Journal of Otolaryngology in 1949 as a scientific Journal published by the Association of Otolaryngologists of India and was later rechristened as IJOHNS to incorporate the changes and progress.
IJOHNS, undoubtedly one of the oldest Journals in India, is the official publication of the Association of Otolaryngologists of India and is about to publish it is 67th Volume in 2015. The Journal published quarterly accepts articles in general Oto-Rhino-Laryngology and various subspecialities such as Otology, Rhinology, Laryngology and Phonosurgery, Neurotology, Head and Neck Surgery etc.
The Journal acts as a window to showcase and project the clinical and research work done by Otolaryngologists community in India and around the world. It is a continued source of useful clinical information with peer review by eminent Otolaryngologists of repute in their respective fields. The Journal accepts articles pertaining to clinical reports, Clinical studies, Research articles in basic and applied Otolaryngology, short Communications, Clinical records reporting unusual presentations or lesions and new surgical techniques. The journal acts as a catalyst and mirrors the Indian Otolaryngologist’s active interests and pursuits. The Journal also invites articles from senior and experienced authors on interesting topics in Otolaryngology and allied sciences from all over the world.
The print version is distributed free to about 4000 members of Association of Otolaryngologists of India and the e-Journal shortly going to make its appearance on the Springer Board can be accessed by all the members.
Association of Otolaryngologists of India and M/s Springer India group have come together to co-publish IJOHNS from January 2007 and this bondage is going to provide an impetus to the Journal in terms of international presence and global exposure.
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