Ceus features of liver pecoma: a case report and literature review.

IF 1.3 Q3 RADIOLOGY, NUCLEAR MEDICINE & MEDICAL IMAGING
Andrea Boccatonda, Marco Marcello Marcellini, Eugenio Ruggeri, Cristina Felicani, Alice Brighenti, Rossella Loiacono, Giorgio Ercolani, Carla Serra
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引用次数: 0

Abstract

Perivascular epithelioid cell neoplasms (PEComas) and epithelioid angiomyolipomas (EAMLs) are two different denominations for the same "mesenchymal tumor composed of histologically and immunohistochemically distinctive perivascular epithelioid cells". Hepatic PEComa/EAML is a very rare neoplasm, and only 29 case reports of hepatic PEComa and 25 of hepatic EAML have been reported in the current literature. A clear female predominance with a mean age at diagnosis of 42.5 years old can be observed by literature review. Ultrasound (US) examination was the first-line diagnostic technique in most of the cases of hepatic PEComa, but it was documented in very few cases of hepatic EAML. A great variability in the ultrasonographic B-mode, color Doppler and contrast-enhanced ultrasonography (CEUS) features of hepatic PEComa/EAML emerges. Computed tomography and magnetic resonance were the most common used techniques to confirm the nature of the hepatic lesion, even if the anatomo-pathological examination was the only technique to display a certainty diagnosis and to differentiate hepatic PEComa/EAML from benign and malignant hepatic lesions. The great majority of hepatic PEComas/EAMLs are surgically treated without any adjuvant therapy.

肝壁细胞瘤的Ceus特征:病例报告和文献综述。
血管周围上皮样细胞瘤(PEComas)和上皮样血管脂肪瘤(EAMLs)是 "由组织学和免疫组织化学上独特的血管周围上皮样细胞组成的间质肿瘤 "的两种不同名称。肝脏上皮细胞瘤/EAML 是一种非常罕见的肿瘤,目前仅有 29 例肝脏上皮细胞瘤和 25 例肝脏 EAML 的文献报道。通过文献回顾可以发现,该患者明显以女性为主,确诊时的平均年龄为 42.5 岁。超声波(US)检查是大多数肝脏长纤维瘤病例的一线诊断技术,但在极少数肝脏 EAML 病例中也有记录。肝PEComa/EAML的超声B型、彩色多普勒和对比增强超声(CEUS)特征存在很大差异。计算机断层扫描和磁共振是确认肝脏病变性质最常用的技术,尽管解剖病理学检查是唯一能显示明确诊断并将肝脏肝纤维瘤/EAML 与肝脏良性和恶性病变区分开来的技术。绝大多数肝脏壁细胞瘤/EAML 都是通过手术治疗的,不需要任何辅助治疗。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
Journal of Ultrasound
Journal of Ultrasound RADIOLOGY, NUCLEAR MEDICINE & MEDICAL IMAGING-
CiteScore
4.10
自引率
15.00%
发文量
133
期刊介绍: The Journal of Ultrasound is the official journal of the Italian Society for Ultrasound in Medicine and Biology (SIUMB). The journal publishes original contributions (research and review articles, case reports, technical reports and letters to the editor) on significant advances in clinical diagnostic, interventional and therapeutic applications, clinical techniques, the physics, engineering and technology of ultrasound in medicine and biology, and in cross-sectional diagnostic imaging. The official language of Journal of Ultrasound is English.
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