Clinicodemographic profile and outcomes of congenital diaphragmatic hernia with sac: experience of a paediatric referral centre.

IF 0.6 Q4 SURGERY
Kardiochirurgia I Torakochirurgia Polska Pub Date : 2024-09-01 Epub Date: 2024-09-24 DOI:10.5114/kitp.2024.143458
Jayalaxmi Shripati Aihole
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引用次数: 0

Abstract

Introduction: Congenital diaphragmatic hernia, in which viscera herniate into the thoracic cavity, is one of the common causes of onset of respiratory distress in neonates and children. Developmentally they may have a sac in rare cases.

Aim: To analyse the clinical profile and the outcome of congenital diaphragmatic hernia with a sac in neonates and children in a paediatric referral centre.

Material and methods: All surgically repaired patients with a congenital diaphragmatic hernia with sac, admitted and treated over a period of sixteen years from January 2005 to December 2021 in a tertiary care referral neonatal and paediatric centre, were included in this study. Forty-three children including neonates were analysed by their clinical characteristics, risk factors and mode of surgical interventions. Congenital diaphragmatic eventration and diaphragmatic hernial defects were excluded from this study.

Results: Forty-three study subjects were grouped into two groups for clinical and statistical analysis, based on their pre-operative and intra-operative findings as well their final diagnosis. Cases of left-sided congenial diaphragmatic hernia with sac (LCDHS) were included in group I (n = 30) and cases of right-sided congenital diaphragmatic hernia with sac (RCDHS) were included in group II (n = 13). Each group was further subclassified into A, B, C according to the age of presentation and side of the lesion in order to determine the prognosis in each subgroup. Level of evidence IV.

Conclusions: Mere awareness and clinical suspicion of such a rare embryological defect - a congenital diaphragmatic hernia with sac - from the attending clinicians can improve the prognosis of affected babies, avoiding morbid consequences if referred early to a tertiary care paediatric and neonatal centre.

带囊先天性膈疝的临床人口学特征和预后:一家儿科转诊中心的经验。
导言先天性膈疝是指内脏疝入胸腔,是导致新生儿和儿童呼吸困难的常见原因之一。目的:分析儿科转诊中心新生儿和儿童先天性膈疝伴囊的临床特征和结果:本研究将 2005 年 1 月至 2021 年 12 月期间在一家三级护理新生儿和儿科转诊中心收治的所有经手术修复的先天性带囊膈疝患者纳入研究范围。研究人员对包括新生儿在内的 43 名患儿的临床特征、风险因素和手术干预方式进行了分析。本研究不包括先天性膈肌分离和膈疝缺损:根据术前、术中检查结果和最终诊断,43 名研究对象被分为两组进行临床和统计分析。左侧先天性膈疝伴囊(LCDHS)病例被分为第一组(30 例),右侧先天性膈疝伴囊(RCDHS)病例被分为第二组(13 例)。根据发病年龄和病变侧将每组进一步细分为 A、B、C 三组,以确定每个亚组的预后。证据等级 IV:临床医生对这种罕见的胚胎缺陷--先天性膈疝伴囊--的认识和临床怀疑可以改善患儿的预后,如果及早转诊到三级儿科和新生儿中心,可以避免病态后果。
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来源期刊
CiteScore
0.90
自引率
14.30%
发文量
44
审稿时长
6-12 weeks
期刊介绍: Polish Journal of Thoracic and Cardiovascular Surgery is a quarterly aimed at cardiologists, cardiosurgeons and thoracic surgeons. Includes the original works (experimental, research and development), illustrative and casuistical works about cardiology and cardiosurgery.
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