Kikuchi-Fujimoto Disease Presenting as Autoimmune Limbic Encephalitis: A Case Report with Review of Literature.

IF 1.9 4区医学 Q3 CLINICAL NEUROLOGY

Annals of Indian Academy of Neurology Pub Date : 2024-10-08 DOI:10.4103/aian.aian_498_24

S B Punith, Ayush Agarwal, Divyani Garg, Ajay Garg, Shamim A Shamim, Saumya Ranjan Mallick, Pranjal Gupta, Achal K Srivastava

引用次数: 0

Abstract

Abstract: Kikuchi-Fujimoto disease (KFD) is a rare benign condition associated with fever and lymphadenopathy and was first described by Kikuchi and Fujimoto independently in 1972 as histiocytic necrotizing lymphadenitis. The diagnosis is made by histopathology with immunohistochemistry. Limbic encephalitis is an extremely rare presentation of this uncommon disease, which has been described mainly in children. Available evidence is sparse in the form of case reports and case series in the form of 10 cases published till date. We report a case of an adult female with KFD with autoimmune limbic encephalitis, who had complete clinical and radiologic recovery with treatment, and a literature review of all the cases published till date.

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表现为自身免疫性边缘脑炎的菊池-藤本氏病：病例报告与文献综述。

摘要：菊池-藤本氏病（Kikuchi-Fujimoto disease，KFD）是一种罕见的良性疾病，伴有发热和淋巴结病变，菊池和藤本于 1972 年首次将其独立描述为组织细胞坏死性淋巴结炎。诊断是通过组织病理学和免疫组化做出的。肢端脑炎是这种不常见疾病的一种极为罕见的表现形式，主要见于儿童。迄今为止，以病例报告和 10 例系列病例形式发表的现有证据非常稀少。我们报告了一例患有 KFD 并伴有自身免疫性边缘脑炎的成年女性患者，该患者经治疗后临床和影像学完全康复，我们还对迄今为止发表的所有病例进行了文献综述。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Annals of Indian Academy of Neurology Nervous System Diseases-

CiteScore

2.20

自引率

11.80%

发文量

293

审稿时长

29 weeks

期刊介绍： The journal has a clinical foundation and has been utilized most by clinical neurologists for improving the practice of neurology. While the focus is on neurology in India, the journal publishes manuscripts of high value from all parts of the world. Journal publishes reviews of various types, original articles, short communications, interesting images and case reports. The journal respects the scientific submission of its authors and believes in following an expeditious double-blind peer review process and endeavors to complete the review process within scheduled time frame. A significant effort from the author and the journal perhaps enables to strike an equilibrium to meet the professional expectations of the peers in the world of scientific publication. AIAN believes in safeguarding the privacy rights of human subjects. In order to comply with it, the journal instructs all authors when uploading the manuscript to also add the ethical clearance (human/animals)/ informed consent of subject in the manuscript. This applies to the study/case report that involves animal/human subjects/human specimens e.g. extracted tooth part/soft tissue for biopsy/in vitro analysis.