A case report of fibromatosis resulting in small bowel obstruction

Danielle Humphries, Teo Fritzke, Felipe Pacheco1, Shravani Sripathi, Daniela Marcano, Akram Alashari
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Abstract

Introduction: Fibromatosis, also known as desmoid tumors, is a benign tumor that is found in patients with a history of familial adenomatous polyposis (FAP) syndrome. Although, sporadic fibromatosis is more common than this classic association. Case Report: This case report describes a 75-year-old woman who was healthy and had no history of familial adenomatous polyposis (FAP). She presented with acute abdominal pain caused by a small bowel obstruction. Computed tomography (CT) imaging demonstrated a solid mass measuring 5 × 5 cm in the left mid-abdomen or the pelvis causing a proximal small bowel obstruction. The patient then underwent an exploratory laparotomy, during which a 45-cm segment of the jejunum, along with associated mesentery and lymph nodes, was resected due to a large mass and extensive adhesions. A primary small bowel anastomosis was performed subsequently. Macroscopic and microscopic pathology evaluations revealed a homogenous mass consistent with fibromatosis, indicating a benign tumor originating from the mesentery. This is an uncommon presentation of small bowel obstruction in an otherwise healthy female patient without a history of FAP. Conclusion: As this case shows, spontaneous fibromatosis can present aggressively and require emergency surgical intervention.
纤维瘤病导致小肠梗阻的病例报告
导言:纤维瘤病又称类粘膜瘤,是一种良性肿瘤,多见于有家族性腺瘤性息肉病(FAP)综合征病史的患者。不过,散发性纤维瘤病比这种典型的关联更为常见。病例报告:本病例报告描述了一名 75 岁的妇女,她身体健康,没有家族性腺瘤性息肉病(FAP)病史。她因小肠梗阻引起急性腹痛而就诊。计算机断层扫描(CT)成像显示,左中腹或盆腔内有一个 5 × 5 厘米的实性肿块,导致近端小肠梗阻。患者随后接受了探查性开腹手术,由于肿块较大且粘连广泛,手术中切除了一段45厘米长的空肠以及相关的肠系膜和淋巴结。随后进行了原发性小肠吻合术。显微镜和显微镜病理评估显示,这是一个与纤维瘤病一致的均质肿块,表明这是一个源自肠系膜的良性肿瘤。这是在一名无 FAP 病史的健康女性患者身上出现的一种罕见的小肠梗阻表现。结论正如本病例所显示的,自发性纤维瘤病的表现可能很凶险,需要紧急手术干预。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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