Monitoring Transcranial Motor-Evoked Potentials in Charcot–Marie–Tooth Disease: A Case Report

Abstract

Charcot–Marie–Tooth (CMT) disease, the most common inherited neuropathy, is the most common neuromuscular disorder. It is associated with several orthopedic deformities. Neurophysiological monitoring during scoliosis surgery in these patients can be challenging due to baseline neurological abnormalities. Intraoperative neuromonitoring (IONM) provides vigilance against postoperative neurological deficits. Literature searches have revealed case reports and studies demonstrating difficulties in obtaining IONM potentials in these patients. This case report shares our experience with IONM using transcranial motor-evoked potentials in a case of CMT disease.