[The Finnish-type congenital nephrotic syndrome. Comments on 2 cases].

Abstract

The authors described the clinical, biologic and histologic particularities of two cases of congenital nephrotic syndrome, Finnish type. Clinically, the hydropic syndrome was represented by anasarca: biologically by marked proteinuria, hypoproteinemia with dysproteinemia and hyperlipemia with dyslipemia. Histologically both cases presented microcystic dilatation of the proximal tubuli contorti. The evolution was unfavorable and ended in death.