Child presenting with a huge cervicofacial mass: about a case report

Q4 Medicine
Oumaima Gabsi, Maha Mejbri, Wassim Frikha, Sara Idriss, Rim Bechraoui, Habiba Mizouni, Najeh Beltaief
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引用次数: 0

Abstract

Introduction: Rhabdomyosarcoma (RMS) is a malignant mesenchymal neoplasm. It is one of the most common malignant head and neck tumors in children and the most frequent soft-tissue sarcoma. The main locations are the base of the skull and the nasopharynx. We present a rare case of a child presenting with parotid RMS. Presentation of Case: A 4-year-old male was admitted to our hospital with the chief complaints of a progressively enlarging, cervicofacial swelling. There was no history of fever or any other constitutional symptoms. Physical examination revealed a 60 mm left cervicofacial swelling, trismus and grade IV left peripheral facial paralysis. There were no fever or palpable nodes. Biological findings showed an increased LDH. Computed tomography scan of the neck revealed a bulky tumor in the left cervicofacial region, involving both superficial and deep lobes of parotid gland, causing compression of oropharynx, extending to the left cervical lymph nodes measuring 77*55 mm with difficulties determining the starting point. Two days after his admission, he presented dyspnea and fever. A tracheotomy was performed associated to cervical biopsy under general anesthesia. The immunohistochemical analysis revealed intense positivity for desmin and myogenin favoring the diagnosis of embryonal rhabdomyosarcoma. The patient received chemotherapy and radiotherapy. A residual mass remained in the parotid region, in contact with the carotid artery. Tumor resection was discussed but ruled out due to high surgical risk. Conclusion: Parotid RMS is a rare entity. Treatment follows a rigorous international protocol associating surgery, chemotherapy and radiation therapy.
儿童颈面部巨大肿块:1例报告
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来源期刊
CiteScore
0.20
自引率
0.00%
发文量
29
期刊介绍: Egyptian Journal of Ear, Nose, Throat and Allied Sciences aspires to play a national, regional and international role in the promotion of responsible and effective research in the field of Otolaryngology, Head and Neck Surgery in Egypt, Middle East and Africa. Mission To encourage and support research in Ear, Nose and Throat (ENT) field and interdisciplinary topics To implement high-quality editorial practices among Otolaryngologists To upgrade the ability and experience of local doctors in international publishing To offer professional publishing support to local researchers, creating a supportive network for career development To highlight ENT diseases and problems peculiar to our region To promote research in endemic, hereditary and infectious ENT problems related to our region To expose and study impact of ethnic, social, environmental and cultural issues on expression of different ENT diseases To organize common epidemiologic research of value to the region To provide resource to national and regional authorities about problems in the field of ENT and their implication on public health and resources To facilitate exchange of knowledge in our part of the world To expand activities with regional and international scientific societies.
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