A very rare case report of late presentation of Moya moya syndrome in a child with history of tubercular meningitis. A case report

Abstract

Moya Moya is a rare idiopathic progressive vaso-occlusive disease characterized by irreversible occlusion of main blood vessels to the brain as they enter into the skull. The occlusive process stimulates the development of an extensive network of enlarged basal, transcortical and transdural collateral vessels. The blockage tends to cause strokes or seizures. The process of narrowing of cerebral vessels seems to be a reaction of brain blood vessels to a wide variety of external stimuli, injuries or genetic defects. We present a case of progressive vasculopathy in a 10 year old girl with history of tuberculous meningitis (TBM) in the infancy and which is being rarely described in pediatric population in which tubercular meningitis is still very much common in this part of world.