Rehabilitation in fibrodysplasia ossificans progressive - experience Report

Abstract

Introduction: Fibrodysplasia Ossificans Progressiva causes gradual limitation of joint range of motion by heterotopic osteogenesis in various connective tissue structures. It is a rare autosomal dominant disease and is correlated with the presence of congenital malformation of the bilateral hallux valgus, presence of ossification that appears spontaneously or precipitated by trauma. Method: The search for the respective titles for FOP and Rehabilitation via a bibliographic review in the Pubmed database, the titles and abstracts were discriminated when they did not bring in their content the treatment of this disease. Results and Discussion: The 9-year-old patient comes with complaints of pain in the joints of the shoulders, elbows, cervical and thoracic spine. Slow walking, structural deformities in the axial axis of the cervico-thoracic spine, decreased shoulder abduction up to 15°, limited elbow flexion and extension. The FOP treatment strategy is a comprehensive program of activities to prevent the myriad possibilities of trauma, from avoiding unnecessary surgical procedures, injections and even biopsies. Dry needling or acupuncture techniques are always contraindicated. Hydrotherapy turns out to be another useful tool in the process of preventing and relieving injuries, contributing to physical conditioning in a safe environment with low impact and cardiopulmonary performance. From the clinical observations, there will be indication of orthoses, auxiliary means for locomotion or adapted wheelchairs. Devices with voice command facilitate some daily activities, encouraging music therapy, dance or theater also favors the well-being of these patients. Conclusion: The disease has some striking characteristics that favor early diagnosis. Injury prevention, medical management of acute painful flare-ups, and rehabilitation are pillars of treatment. There is still no curative treatment, however, the determination of a therapeutic plan prevents future trauma and can guarantee an adequate prognosis even though it is difficult and full of functional limitations for patients.